| Fibroblast growth factor 21 drives dynamics of local and systemic stress responses in mitochondrial myopathy with mtDNA deletions S Forsström, CB Jackson, CJ Carroll, M Kuronen, E Pirinen, S Pradhan, ... Cell metabolism 30 (6), 1040-1054. e7, 2019 | 206 | 2019 |
| Phage-Type RNA Polymerase RPOTmp Performs Gene-Specific Transcription in Mitochondria of Arabidopsis thaliana K Kuhn, U Richter, EH Meyer, E Delannoy, A Falcon de Longevialle, ... The Plant Cell 21 (9), 2762-2779, 2009 | 165 | 2009 |
| A mitochondrial ribosomal and RNA decay pathway blocks cell proliferation U Richter, T Lahtinen, P Marttinen, M Myöhänen, D Greco, G Cannino, ... Current Biology 23 (6), 535-541, 2013 | 137 | 2013 |
| Mechanism of membrane-tethered mitochondrial protein synthesis Y Itoh, J Andréll, A Choi, U Richter, P Maiti, RB Best, A Barrientos, ... Science 371 (6531), 846-849, 2021 | 125 | 2021 |
| Whole-exome sequencing identifies a mutation in the mitochondrial ribosome protein MRPL44 to underlie mitochondrial infantile cardiomyopathy CJ Carroll, P Isohanni, R Pöyhönen, L Euro, U Richter, V Brilhante, A Götz, ... Journal of medical genetics 50 (3), 151-159, 2013 | 121 | 2013 |
| Quality control of mitochondrial protein synthesis is required for membrane integrity and cell fitness U Richter, T Lahtinen, P Marttinen, F Suomi, BJ Battersby Journal of Cell Biology 211 (2), 373-389, 2015 | 120 | 2015 |
| Two RpoT genes of Physcomitrella patens encode phage-type RNA polymerases with dual targeting to mitochondria and plastids U Richter, J Kiessling, B Hedtke, E Decker, R Reski, T Börner, A Weihe Gene 290 (1-2), 95-105, 2002 | 97 | 2002 |
| RNA modification landscape of the human mitochondrial tRNALys regulates protein synthesis U Richter, ME Evans, WC Clark, P Marttinen, EA Shoubridge, ... Nature communications 9 (1), 3966, 2018 | 93 | 2018 |
| Defective mitochondrial RNA processing due to PNPT1 variants causes Leigh syndrome S Matilainen, CJ Carroll, U Richter, L Euro, M Pohjanpelto, A Paetau, ... Human molecular genetics 26 (17), 3352-3361, 2017 | 59 | 2017 |
| Coibamide A targets Sec61 to prevent biogenesis of secretory and membrane proteins D Tranter, AO Paatero, S Kawaguchi, S Kazemi, JD Serrill, J Kellosalo, ... ACS chemical biology 15 (8), 2125-2136, 2020 | 52 | 2020 |
| Why translation counts for mitochondria–retrograde signalling links mitochondrial protein synthesis to mitochondrial biogenesis and cell proliferation BJ Battersby, U Richter Journal of cell science 126 (19), 4331-4338, 2013 | 52 | 2013 |
| The molecular pathology of pathogenic mitochondrial tRNA variants U Richter, R McFarland, RW Taylor, SJ Pickett FEBS letters 595 (8), 1003-1024, 2021 | 44 | 2021 |
| A variant in MRPS14 (uS14m) causes perinatal hypertrophic cardiomyopathy with neonatal lactic acidosis, growth retardation, dysmorphic features and … CB Jackson, M Huemer, R Bolognini, F Martin, G Szinnai, BC Donner, ... Human molecular genetics 28 (4), 639-649, 2019 | 44 | 2019 |
| A mitochondrial rRNA dimethyladenosine methyltransferase in Arabidopsis U Richter, K Kühn, S Okada, A Brennicke, A Weihe, T Börner The Plant Journal 61 (4), 558-569, 2010 | 40 | 2010 |
| Mitochondrial stress response triggered by defects in protein synthesis quality control U Richter, KY Ng, F Suomi, P Marttinen, T Turunen, C Jackson, ... Life science alliance 2 (1), 2019 | 39 | 2019 |
| A novel mitochondrial ATP6 frameshift mutation causing isolated complex V deficiency, ataxia and encephalomyopathy CB Jackson, D Hahn, B Schröter, U Richter, BJ Battersby, ... European journal of medical genetics 60 (6), 345-351, 2017 | 32 | 2017 |
| Splicing defect in mitochondrial Seryl‐tRNA synthetase gene causes progressive spastic paresis instead of HUPRA syndrome T Linnankivi, N Neupane, U Richter, P Isohanni, H Tyynismaa Human mutation 37 (9), 884-888, 2016 | 32 | 2016 |
| Mice harbouring a SCA28 patient mutation in AFG3L2 develop late-onset ataxia associated with enhanced mitochondrial proteotoxicity C Mancini, E Hoxha, L Iommarini, A Brussino, U Richter, F Montarolo, ... Neurobiology of disease 124, 14-28, 2019 | 30 | 2019 |
| Evolution of plant phage-type RNA polymerases: the genome of the basal angiosperm Nuphar advena encodes two mitochondrial and one plastid phage-type RNA … C Yin, U Richter, T Börner, A Weihe BMC Evolutionary Biology 10, 1-10, 2010 | 28 | 2010 |
| Evolution of Phage-Type RNA Polymerases in Higher Plants: Characterization of the Single Phage-Type RNA Polymerase Gene from Selaginella moellendorffii C Yin, U Richter, T Börner, A Weihe Journal of molecular evolution 68, 528-538, 2009 | 18 | 2009 |
