Efficient mitochondrial biogenesis drives incomplete penetrance in Leber’s hereditary optic neuropathy C Giordano, L Iommarini, L Giordano, A Maresca, A Pisano, ML Valentino, ... Brain 137 (2), 335-353, 2014 | 313 | 2014 |
Oestrogens ameliorate mitochondrial dysfunction in Leber’s hereditary optic neuropathy C Giordano, M Montopoli, E Perli, M Orlandi, M Fantin, FN Ross-Cisneros, ... Brain 134 (1), 220-234, 2011 | 284 | 2011 |
Cardiac involvement in mitochondrial DNA disease: clinical spectrum, diagnosis, and management MGD Bates, JP Bourke, C Giordano, G d'Amati, DM Turnbull, RW Taylor European heart journal 33 (24), 3023-3033, 2012 | 255 | 2012 |
A homoplasmic mitochondrial transfer ribonucleic acid mutation as a cause of maternally inherited hypertrophic cardiomyopathy RW Taylor, C Giordano, MM Davidson, G d’Amati, H Bain, CM Hayes, ... Journal of the American College of Cardiology 41 (10), 1786-1796, 2003 | 219 | 2003 |
Induction of mitochondrial biogenesis is a maladaptive mechanism in mitochondrial cardiomyopathies M Sebastiani, C Giordano, C Nediani, C Travaglini, E Borchi, M Zani, ... Journal of the American College of Cardiology 50 (14), 1362-1369, 2007 | 218 | 2007 |
Pathogenic expression of homoplasmic mtDNA mutations needs a complex nuclear–mitochondrial interaction V Carelli, C Giordano, G d'Amati TRENDS in Genetics 19 (5), 257-262, 2003 | 175 | 2003 |
Cigarette toxicity triggers Leber’s hereditary optic neuropathy by affecting mtDNA copy number, oxidative phosphorylation and ROS detoxification pathways L Giordano, S Deceglie, P d'Adamo, ML Valentino, C La Morgia, ... Cell death & disease 6 (12), e2021-e2021, 2015 | 144 | 2015 |
Inhibition of glucose-6-phosphate dehydrogenase sensitizes cisplatin-resistant cells to death D Catanzaro, E Gaude, G Orso, C Giordano, G Guzzo, A Rasola, ... Oncotarget 6 (30), 30102, 2015 | 134 | 2015 |
Gastrointestinal dysmotility in mitochondrial neurogastrointestinal encephalomyopathy is caused by mitochondrial DNA depletion C Giordano, M Sebastiani, R De Giorgio, C Travaglini, A Tancredi, ... The American journal of pathology 173 (4), 1120-1128, 2008 | 131 | 2008 |
Diagnosis of myocardial infarction at autopsy: AECVP reappraisal in the light of the current clinical classification K Michaud, C Basso, G d’Amati, C Giordano, I Kholová, SD Preston, ... Virchows Archiv 476, 179-194, 2020 | 129 | 2020 |
Enhanced ROS production by NADPH oxidase is correlated to changes in antioxidant enzyme activity in human heart failure E Borchi, V Bargelli, F Stillitano, C Giordano, M Sebastiani, PA Nassi, ... Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1802 (3), 331-338, 2010 | 129 | 2010 |
Myocyte transdifferentiation: a possible pathogenetic mechanism for arrhythmogenic right ventricular cardiomyopathy G d'Amati, CRT di Gioia, C Giordano, P Gallo Archives of pathology & laboratory medicine 124 (2), 287-290, 2000 | 122 | 2000 |
Pantothenate kinase-associated neurodegeneration: altered mitochondria membrane potential and defective respiration in Pank2 knock-out mouse model D Brunetti, S Dusi, M Morbin, A Uggetti, F Moda, I D'Amato, C Giordano, ... Human molecular genetics 21 (24), 5294-5305, 2012 | 121 | 2012 |
Pantethine treatment is effective in recovering the disease phenotype induced by ketogenic diet in a pantothenate kinase-associated neurodegeneration mouse model D Brunetti, S Dusi, C Giordano, C Lamperti, M Morbin, V Fugnanesi, ... Brain 137 (1), 57-68, 2014 | 109 | 2014 |
Impaired mitochondrial biogenesis is a common feature to myocardial hypertrophy and end-stage ischemic heart failure A Pisano, B Cerbelli, E Perli, M Pelullo, V Bargelli, C Preziuso, M Mancini, ... Cardiovascular Pathology 25 (2), 103-112, 2016 | 96 | 2016 |
Targeting estrogen receptor β as preventive therapeutic strategy for Leber's hereditary optic neuropathy A Pisano, C Preziuso, L Iommarini, E Perli, P Grazioli, AF Campese, ... Human molecular genetics 24 (24), 6921-6931, 2015 | 87 | 2015 |
TTC19 Plays a Husbandry Role on UQCRFS1 Turnover in the Biogenesis of Mitochondrial Respiratory Complex III. ZM Bottani E, Cerutti R, Harbour ME, Ravaglia S, Dogan SA, Giordano C ... Mol Cell. 67 (1), 96-105, 2017 | 86 | 2017 |
Causes of late failure after heart transplantation: a ten-year survey. P Gallo, L Agozzino, A Angelini, E Arbustini, G Bartoloni, P Bernucci, ... The Journal of heart and lung transplantation: the official publication of …, 1997 | 85 | 1997 |
Small-fibre neuropathy related to bulbar and spinal-onset in patients with ALS A Truini, A Biasiotta, E Onesti, G Di Stefano, M Ceccanti, S La Cesa, ... Journal of neurology 262, 1014-1018, 2015 | 82 | 2015 |
NADPH oxidase-dependent redox signaling in human heart failure: relationship between the left and right ventricle C Nediani, E Borchi, C Giordano, S Baruzzo, V Ponziani, M Sebastiani, ... Journal of molecular and cellular cardiology 42 (4), 826-834, 2007 | 78 | 2007 |