miR-21 and 221 upregulation and miR-181b downregulation in human grade II–IV astrocytic tumors A Conti, MH Aguennouz, D La Torre, C Tomasello, S Cardali, FF Angileri, ... Journal of neuro-oncology 93, 325-332, 2009 | 297 | 2009 |
Activation of nuclear factor-κB in inflammatory myopathies and Duchenne muscular dystrophy MC Monici, M Aguennouz, A Mazzeo, C Messina, G Vita Neurology 60 (6), 993-997, 2003 | 234 | 2003 |
Clinical, molecular, and protein correlations in a large sample of genetically diagnosed Italian limb girdle muscular dystrophy patients M Guglieri, F Magri, MG D'Angelo, A Prelle, L Morandi, C Rodolico, ... Human mutation 29 (2), 258-266, 2008 | 228 | 2008 |
AMPA receptor GluA2 subunit defects are a cause of neurodevelopmental disorders V Salpietro, CL Dixon, H Guo, OD Bello, J Vandrovcova, S Efthymiou, ... Nature communications 10 (1), 3094, 2019 | 225 | 2019 |
Nuclear factor kappa-B blockade reduces skeletal muscle degeneration and enhances muscle function in Mdx mice S Messina, A Bitto, M Aguennouz, L Minutoli, MC Monici, D Altavilla, ... Experimental neurology 198 (1), 234-241, 2006 | 192 | 2006 |
Matrix metalloproteinase 9 and transglutaminase 2 expression at the ocular surface in patients with different forms of dry eye disease P Aragona, MH Aguennouz, L Rania, E Postorino, MS Sommario, ... Ophthalmology 122 (1), 62-71, 2015 | 160 | 2015 |
Lipid peroxidation inhibition blunts nuclear factor-κB activation, reduces skeletal muscle degeneration, and enhances muscle function in mdx mice S Messina, D Altavilla, M Aguennouz, P Seminara, L Minutoli, MC Monici, ... The American journal of pathology 168 (3), 918-926, 2006 | 155 | 2006 |
VEGF overexpression via adeno‐associated virus gene transfer promotes skeletal muscle regeneration and enhances muscle function in mdx mice S Messina, A Mazzeo, A Bitto, M Aguennouz, A Migliorato, ... The FASEB journal 21 (13), 3737-3746, 2007 | 125 | 2007 |
Nuclear factor‐κB activation and differential expression of survivin and Bcl‐2 in human grade 2–4 astrocytomas FF Angileri, MH Aguennouz, A Conti, D La Torre, S Cardali, R Crupi, ... Cancer 112 (10), 2258-2266, 2008 | 123 | 2008 |
Activation of NF-kB pathway in Duchenne muscular dystrophy: relation to age S MESSINA, GL Vita, M Aguennouz, M Sframeli, S Romeo, C Rodolico, ... Acta myologica 30 (1), 16, 2011 | 120 | 2011 |
Mutation finding in patients with dysferlin deficiency and role of the dysferlin interacting proteins annexin A1 and A2 in muscular dystrophies R Cagliani, F Magri, A Toscano, L Merlini, F Fortunato, C Lamperti, ... Human mutation 26 (3), 283-283, 2005 | 102 | 2005 |
Mutations in the neuronal vesicular SNARE VAMP2 affect synaptic membrane fusion and impair human neurodevelopment V Salpietro, NT Malintan, I Llano-Rivas, CG Spaeth, S Efthymiou, ... The American Journal of Human Genetics 104 (4), 721-730, 2019 | 96 | 2019 |
Influence of dietary habits on oxidative stress markers in Hashimoto's thyroiditis RM Ruggeri, S Giovinazzo, MC Barbalace, M Cristani, A Alibrandi, ... Thyroid 31 (1), 96-105, 2021 | 88 | 2021 |
Flavocoxid counteracts muscle necrosis and improves functional properties in mdx mice: a comparison study with methylprednisolone S Messina, A Bitto, M Aguennouz, A Mazzeo, A Migliorato, F Polito, ... Experimental neurology 220 (2), 349-358, 2009 | 82 | 2009 |
PDXK mutations cause polyneuropathy responsive to pyridoxal 5′‐phosphate supplementation V Chelban, MP Wilson, J Warman Chardon, J Vandrovcova, MN Zanetti, ... Annals of neurology 86 (2), 225-240, 2019 | 75 | 2019 |
RAGE‐NF‐κB pathway activation in response to oxidative stress in facioscapulohumeral muscular dystrophy V Macaione, M Aguennouz, C Rodolico, A Mazzeo, A Patti, E Cannistraci, ... Acta Neurologica Scandinavica 115 (2), 115-121, 2007 | 75 | 2007 |
Clinical features and new molecular findings in carnitine palmitoyltransferase II (CPT II) deficiency S Corti, A Bordoni, D Ronchi, O Musumeci, M Aguennouz, A Toscano, ... Journal of the neurological sciences 266 (1-2), 97-103, 2008 | 71 | 2008 |
Clinical features and new molecular findings in muscle phosphofructokinase deficiency (GSD type VII) O Musumeci, C Bruno, T Mongini, C Rodolico, M Aguennouz, E Barca, ... Neuromuscular Disorders 22 (4), 325-330, 2012 | 62 | 2012 |
Role of inflammation and oxidative stress mediators in gliomas A Conti, C Gulì, D La Torre, C Tomasello, FF Angileri, MH Aguennouz Cancers 2 (2), 693-712, 2010 | 62 | 2010 |
Limb-girdle myasthenia: clinical, electrophysiological and morphological features in familial and autoimmune cases C Rodolico, A Toscano, M Autunno, S Messina, C Nicolosi, M Aguennouz, ... Neuromuscular Disorders 12 (10), 964-969, 2002 | 62 | 2002 |