Hsp70 chaperones: cellular functions and molecular mechanism

MP Mayer, B Bukau - Cellular and molecular life sciences, 2005 - Springer
Hsp70 proteins are central components of the cellular network of molecular chaperones and
folding catalysts. They assist a large variety of protein folding processes in the cell by …

Protein aggregation and aggregate toxicity: new insights into protein folding, misfolding diseases and biological evolution

M Stefani, CM Dobson - Journal of molecular medicine, 2003 - Springer
The deposition of proteins in the form of amyloid fibrils and plaques is the characteristic
feature of more than 20 degenerative conditions affecting either the central nervous system …

Molecular mechanisms and potential therapeutical targets in Huntington's disease

C Zuccato, M Valenza, E Cattaneo - Physiological reviews, 2010 - journals.physiology.org
Huntington's disease (HD) is a neurodegenerative disorder caused by a CAG repeat
expansion in the gene encoding for huntingtin protein. A lot has been learned about this …

Protein homeostasis and aging: The importance of exquisite quality control

H Koga, S Kaushik, AM Cuervo - Ageing research reviews, 2011 - Elsevier
All cells count on precise mechanisms that regulate protein homeostasis to maintain a stable
and functional proteome. A progressive deterioration in the ability of cells to preserve the …

Cellular strategies of protein quality control

B Chen, M Retzlaff, T Roos… - Cold Spring Harbor …, 2011 - cshperspectives.cshlp.org
Eukaryotic cells must contend with a continuous stream of misfolded proteins that
compromise the cellular protein homeostasis balance and jeopardize cell viability. An …

A molecular chaperone breaks the catalytic cycle that generates toxic Aβ oligomers

SIA Cohen, P Arosio, J Presto… - Nature structural & …, 2015 - nature.com
Alzheimer's disease is an increasingly prevalent neurodegenerative disorder whose
pathogenesis has been associated with aggregation of the amyloid-β peptide (Aβ42) …

Hsp70 reduces α-synuclein aggregation and toxicity

J Klucken, Y Shin, E Masliah, BT Hyman… - Journal of Biological …, 2004 - ASBMB
Aggregation and cytotoxicity of misfolded α-synuclein is postulated to be crucial in the
disease process of neurodegenerative disorders such as Parkinson's disease and DLB …

Polyglutamine (PolyQ) Diseases: Navigating the Landscape of Neurodegeneration

R Tenchov, JM Sasso, QA Zhou - ACS Chemical Neuroscience, 2024 - ACS Publications
Polyglutamine (polyQ) diseases are a group of inherited neurodegenerative disorders
caused by expanded cytosine-adenine-guanine (CAG) repeats encoding proteins with …

Hormetic heat stress and HSF-1 induce autophagy to improve survival and proteostasis in C. elegans

C Kumsta, JT Chang, J Schmalz, M Hansen - Nature communications, 2017 - nature.com
Stress-response pathways have evolved to maintain cellular homeostasis and to ensure the
survival of organisms under changing environmental conditions. Whereas severe stress is …

Huntingtin and the molecular pathogenesis of Huntington's disease: Fourth in Molecular Medicine Review Series

C Landles, GP Bates - EMBO reports, 2004 - embopress.org
Huntington's disease (HD) is a late-onset neurodegenerative disorder that is caused by a
CAG repeat expansion in the IT15 gene, which results in a long stretch of polyglutamine …