[HTML][HTML] ECFS best practice guidelines: the 2018 revision

C Castellani, AJA Duff, SC Bell, HGM Heijerman… - Journal of cystic …, 2018 - Elsevier
Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …

[HTML][HTML] European cystic fibrosis society standards of care: best practice guidelines

AR Smyth, SC Bell, S Bojcin, M Bryon, A Duff… - Journal of cystic …, 2014 - Elsevier
Specialised CF care has led to a dramatic improvement in survival in CF: in the last four
decades, well above what was seen in the general population over the same period. With …

Role of CFTR in epithelial physiology

V Saint-Criq, MA Gray - Cellular and Molecular Life Sciences, 2017 - Springer
Salt and fluid absorption and secretion are two processes that are fundamental to epithelial
function and whole body fluid homeostasis, and as such are tightly regulated in epithelial …

[HTML][HTML] Evaluation and management of acute pancreatitis

AT Chatila, M Bilal, P Guturu - World journal of clinical cases, 2019 - ncbi.nlm.nih.gov
Acute pancreatitis (AP) is one of the most common gastrointestinal causes for hospi-
talization in the United States. In 2015, AP accounted for approximately 390000 …

Cystic fibrosis from the gastroenterologist's perspective

CY Ooi, PR Durie - Nature reviews Gastroenterology & hepatology, 2016 - nature.com
Cystic fibrosis is a life-limiting, recessive disease caused by mutations in the cystic fibrosis
transmembrane conductance regulator (CFTR) gene. Increased survival outcomes and the …

Diabetes of the exocrine pancreas

K Wynne, B Devereaux… - … of Gastroenterology and …, 2019 - Wiley Online Library
Diabetes of the exocrine pancreas (DEP) is a form of diabetes that occurs due to pancreatic
disease. It is far more common than has been previously considered, with a recent study …

Correlating cystic fibrosis transmembrane conductance regulator function with clinical features to inform precision treatment of cystic fibrosis

AF McCague, KS Raraigh, MJ Pellicore… - American journal of …, 2019 - atsjournals.org
Rationale: The advent of precision treatment for cystic fibrosis using small-molecule
therapeutics has created a need to estimate potential clinical improvements attributable to …

Features of severe liver disease with portal hypertension in patients with cystic fibrosis

JR Stonebraker, CY Ooi, RG Pace, H Corvol… - Clinical …, 2016 - Elsevier
Background & Aims Liver disease is the third leading cause of death in patients with cystic
fibrosis (CF), but features of patients with CF, severe liver disease, and portal hypertension …

Hereditary pancreatitis: current perspectives

KL Raphael, FF Willingham - Clinical and experimental …, 2016 - Taylor & Francis
Hereditary pancreatitis (HP) is a rare cause of acute, recurrent acute, and chronic
pancreatitis. It may present similarly to other causes of acute and chronic pancreatitis, and …

Multicenter prospective study showing a high gastrointestinal symptom burden in cystic fibrosis

B Moshiree, AJ Freeman, PT Vu, U Khan… - Journal of Cystic …, 2023 - Elsevier
Background and aims People with cystic fibrosis (PwCF) suffer from gastrointestinal (GI)
symptoms affecting their quality of life (QOL). Despite the relevance of GI symptoms to the …