[HTML][HTML] ECFS best practice guidelines: the 2018 revision
Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …
[HTML][HTML] European cystic fibrosis society standards of care: best practice guidelines
Specialised CF care has led to a dramatic improvement in survival in CF: in the last four
decades, well above what was seen in the general population over the same period. With …
decades, well above what was seen in the general population over the same period. With …
Role of CFTR in epithelial physiology
Salt and fluid absorption and secretion are two processes that are fundamental to epithelial
function and whole body fluid homeostasis, and as such are tightly regulated in epithelial …
function and whole body fluid homeostasis, and as such are tightly regulated in epithelial …
[HTML][HTML] Evaluation and management of acute pancreatitis
Acute pancreatitis (AP) is one of the most common gastrointestinal causes for hospi-
talization in the United States. In 2015, AP accounted for approximately 390000 …
talization in the United States. In 2015, AP accounted for approximately 390000 …
Cystic fibrosis from the gastroenterologist's perspective
CY Ooi, PR Durie - Nature reviews Gastroenterology & hepatology, 2016 - nature.com
Cystic fibrosis is a life-limiting, recessive disease caused by mutations in the cystic fibrosis
transmembrane conductance regulator (CFTR) gene. Increased survival outcomes and the …
transmembrane conductance regulator (CFTR) gene. Increased survival outcomes and the …
Diabetes of the exocrine pancreas
Diabetes of the exocrine pancreas (DEP) is a form of diabetes that occurs due to pancreatic
disease. It is far more common than has been previously considered, with a recent study …
disease. It is far more common than has been previously considered, with a recent study …
Correlating cystic fibrosis transmembrane conductance regulator function with clinical features to inform precision treatment of cystic fibrosis
Rationale: The advent of precision treatment for cystic fibrosis using small-molecule
therapeutics has created a need to estimate potential clinical improvements attributable to …
therapeutics has created a need to estimate potential clinical improvements attributable to …
Features of severe liver disease with portal hypertension in patients with cystic fibrosis
Background & Aims Liver disease is the third leading cause of death in patients with cystic
fibrosis (CF), but features of patients with CF, severe liver disease, and portal hypertension …
fibrosis (CF), but features of patients with CF, severe liver disease, and portal hypertension …
Hereditary pancreatitis: current perspectives
KL Raphael, FF Willingham - Clinical and experimental …, 2016 - Taylor & Francis
Hereditary pancreatitis (HP) is a rare cause of acute, recurrent acute, and chronic
pancreatitis. It may present similarly to other causes of acute and chronic pancreatitis, and …
pancreatitis. It may present similarly to other causes of acute and chronic pancreatitis, and …
Multicenter prospective study showing a high gastrointestinal symptom burden in cystic fibrosis
Background and aims People with cystic fibrosis (PwCF) suffer from gastrointestinal (GI)
symptoms affecting their quality of life (QOL). Despite the relevance of GI symptoms to the …
symptoms affecting their quality of life (QOL). Despite the relevance of GI symptoms to the …