[HTML][HTML] Immunogenetic Landscape in Pediatric Common Variable Immunodeficiency

A Szczawińska-Popłonyk, W Ciesielska… - International Journal of …, 2024‏ - mdpi.com
Common variable immunodeficiency (CVID) is the most common symptomatic antibody
deficiency, characterized by heterogeneous genetic, immunological, and clinical …

Common variable immunodeficiency, cross currents, and prevailing winds

N Romberg, C Le Coz - Immunological Reviews, 2024‏ - Wiley Online Library
Common variable immunodeficiency (CVID) is a heterogenous disease category created to
distinguish late‐onset antibody deficiencies from early‐onset diseases like …

Cytokine dysregulation despite immunoglobulin replacement therapy in common variable immunodeficiency (CVID)

R Poto, A Pecoraro, AL Ferrara, A Punziano… - Frontiers in …, 2023‏ - frontiersin.org
Introduction Common variable immunodeficiency (CVID) is the most prevalent symptomatic
primary immunodeficiency. CVID is a heterogeneous disorder with a presumed multifactorial …

Response to severe acute respiratory syndrome coronavirus 2 initial series and additional dose vaccine in patients with predominant antibody deficiency

S Barmettler, DV DiGiacomo, NJ Yang, T Lam… - The Journal of Allergy …, 2022‏ - Elsevier
Background Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2) infection in
patients with predominant antibody deficiency (PAD) is associated with high morbidity, yet …

Convergence of cytokine dysregulation and antibody deficiency in common variable immunodeficiency with inflammatory complications

ML Abyazi, KA Bell, G Gyimesi, TS Baker… - Journal of Allergy and …, 2022‏ - Elsevier
Background Noninfectious complications are the greatest cause of morbidity and mortality in
common variable immunodeficiency (CVID), but their pathogenesis remains poorly defined …

Is there a role for microbiome-based approach in common variable immunodeficiency?

R Poto, G Laniro, A de Paulis, G Spadaro… - Clinical and …, 2023‏ - Springer
Common variable immunodeficiency (CVID) is a primary immunodeficiency characterized by
low levels of serum immunoglobulins and increased susceptibility to infections, autoimmune …

Case 20-2024: A 73-Year-Old Man with Recurrent Fever and Liver Lesions

L Ganapathi, RL Cochran, GK Robbins… - … England Journal of …, 2024‏ - Mass Medical Soc
Case 20-2024: A 73-Year-Old Man with Recurrent Fever and Liver Lesions | New England Journal
of Medicine Skip to main content The New England Journal of Medicine homepage Advanced …

Response to SARS-CoV-2 initial series and additional dose vaccine in pediatric patients with predominantly antibody deficiency

M Tandon, DV DiGiacomo, B Zhou… - Frontiers in …, 2023‏ - frontiersin.org
Data regarding response to SARS-CoV-2 immunization in pediatric patients with
predominantly antibody deficiency (PAD) is limited. We evaluated SARS-CoV-2 …

Immune dysregulation in pediatric common variable immunodeficiency: implications for the diagnostic approach

A Szczawińska-Popłonyk, K Ta̧polska-Jóźwiak… - Frontiers in …, 2022‏ - frontiersin.org
Infections and infectious complications are hallmarks of common variable immunodeficiency
(CVID) and the leading cause of morbidity and mortality in affected patients at any age …

A Cross-Sectional Study of Health-Related Quality of Life in Patients with Predominantly Antibody Deficiency

A Elmoursi, B Zhou, MS Ong, JS Hong, A Pak… - Journal of clinical …, 2024‏ - Springer
Health-related quality of life (HRQoL) measures individual well-being across physical,
psychological, and social domains. Patients with predominantly antibody deficiency (PAD) …