Background Nutritional status is paramount in Cystic Fibrosis (CF) and is directly correlated
with morbidity and mortality. The first ESPEN-ESPGHAN-ECFS guidelines on nutrition care …

Cystic fibrosis bone disease (CFBD) is a common long-term complication of cystic fibrosis
(CF) that can lead to increased fractures and significant morbidity and mortality in this patient …

Cystic fibrosis is a monogenic disease with a multisystemic phenotype, ranging from
predisposition to chronic lung infection and inflammation to reduced bone mass. The exact …

Background Osteoporosis is a bone mineralisation disorder occurring in about one third of
adults with cystic fibrosis. Bisphosphonates can increase bone mineral density and …

Context Cystic fibrosis (CF) transmembrane conductance (CFTR) dysfunction may play a
role in CF-related bone disease (CFBD). Ivacaftor is a CFTR potentiator effective in …

With increasing life expectancy in people with Cystic fibrosis (CF), the focus of clinical care
has shifted to management and prevention of non-pulmonary comorbidities. CF related …

Current Opinion in Pulmonary Medicine Log in or Register Subscribe to journalSubscribe
Get new issue alertsGet alerts Secondary Logo Journal Logo Advanced Search Toggle …

Cystic fibrosis (CF) is a genetic condition primarily affecting the respiratory system, with the
associated progressive lung damage and loss of function resulting in reduced lifespan …

Background Osteoporosis is a disorder of bone mineralisation occurring in about one third of
adults with cystic fibrosis. Bisphosphonates can increase bone mineral density and …

Background The lack of cystic fibrosis transmembrane conductance regulator (CFTR)
function causes cystic fibrosis (CF), predisposing to severe lung disease, reduced growth …