Small-molecule fluorogenic probes for mitochondrial nanoscale imaging

R Zhai, B Fang, Y Lai, B Peng, H Bai, X Liu… - Chemical Society …, 2023 - pubs.rsc.org
Mitochondria are inextricably linked to the development of diseases and cell metabolism
disorders. Super-resolution imaging (SRI) is crucial in enhancing our understanding of …

Mechanisms of replication and repair in mitochondrial DNA deletion formation

GA Fontana, HL Gahlon - Nucleic acids research, 2020 - academic.oup.com
Deletions in mitochondrial DNA (mtDNA) are associated with diverse human pathologies
including cancer, aging and mitochondrial disorders. Large-scale deletions span kilobases …

Clinical implementation of RNA sequencing for Mendelian disease diagnostics

VA Yépez, M Gusic, R Kopajtich, C Mertes, NH Smith… - Genome medicine, 2022 - Springer
Background Lack of functional evidence hampers variant interpretation, leaving a large
proportion of individuals with a suspected Mendelian disorder without genetic diagnosis …

Regulation of mammalian mitochondrial dynamics: opportunities and challenges

R Yu, U Lendahl, M Nistér, J Zhao - Frontiers in endocrinology, 2020 - frontiersin.org
Mitochondria are highly dynamic organelles and important for a variety of cellular functions.
They constantly undergo fission and fusion events, referred to as mitochondrial dynamics …

The impact of HIV-and ART-induced mitochondrial dysfunction in cellular senescence and aging

M Schank, J Zhao, JP Moorman, ZQ Yao - Cells, 2021 - mdpi.com
According to the WHO, 38 million individuals were living with human immunodeficiency virus
(HIV), 25.4 million of which were using antiretroviral therapy (ART) at the end of 2019 …

Mitochondrial energy generation disorders: genes, mechanisms, and clues to pathology

AE Frazier, DR Thorburn, AG Compton - Journal of Biological Chemistry, 2019 - ASBMB
Inherited disorders of oxidative phosphorylation cause the clinically and genetically
heterogeneous diseases known as mitochondrial energy generation disorders, or …

Therapies for mitochondrial diseases and current clinical trials

AW El-Hattab, AM Zarante, M Almannai… - Molecular genetics and …, 2017 - Elsevier
Mitochondrial diseases are a clinically and genetically heterogeneous group of disorders
that result from dysfunction of the mitochondrial oxidative phosphorylation due to molecular …

Metabolism and innate immunity meet at the mitochondria

A Bahat, T MacVicar, T Langer - Frontiers in Cell and Developmental …, 2021 - frontiersin.org
Mitochondria are master regulators of metabolism and have emerged as key signalling
organelles of the innate immune system. Each mitochondrion harbours potent agonists of …

Mitochondrial fission and fusion: molecular mechanisms, biological functions, and related disorders

M Al Ojaimi, A Salah, AW El-Hattab - Membranes, 2022 - mdpi.com
Mitochondria are dynamic organelles that undergo fusion and fission. These active
processes occur continuously and simultaneously and are mediated by nuclear-DNA …

Mitochondrial dynamics: Biological roles, molecular machinery, and related diseases

AW El-Hattab, J Suleiman, M Almannai… - Molecular Genetics and …, 2018 - Elsevier
Mitochondria are dynamic organelles that undergo fusion, fission, movement, and
mitophagy. These processes are essential to maintain the normal mitochondrial …