Neuropathology and molecular diagnosis of Synucleinopathies

S Koga, H Sekiya, N Kondru, OA Ross… - Molecular …, 2021‏ - Springer
Synucleinopathies are clinically and pathologically heterogeneous disorders characterized
by pathologic aggregates of α-synuclein in neurons and glia, in the form of Lewy bodies …

The expanding amyloid family: Structure, stability, function, and pathogenesis

MR Sawaya, MP Hughes, JA Rodriguez, R Riek… - Cell, 2021‏ - cell.com
The hidden world of amyloid biology has suddenly snapped into atomic-level focus,
revealing over 80 amyloid protein fibrils, both pathogenic and functional. Unlike globular …

Structures of α-synuclein filaments from human brains with Lewy pathology

Y Yang, Y Shi, M Schweighauser, X Zhang, A Kotecha… - Nature, 2022‏ - nature.com
Parkinson's disease (PD) is the most common movement disorder, with resting tremor,
rigidity, bradykinesia and postural instability being major symptoms. Neuropathologically, it …

Discriminating α-synuclein strains in Parkinson's disease and multiple system atrophy

M Shahnawaz, A Mukherjee, S Pritzkow, N Mendez… - Nature, 2020‏ - nature.com
Synucleinopathies are neurodegenerative diseases that are associated with the misfolding
and aggregation of α-synuclein, including Parkinson's disease, dementia with Lewy bodies …

Protein transmission in neurodegenerative disease

C Peng, JQ Trojanowski, VMY Lee - Nature Reviews Neurology, 2020‏ - nature.com
Most neurodegenerative diseases are characterized by the intracellular or extracellular
aggregation of misfolded proteins such as amyloid-β and tau in Alzheimer disease, α …

Structures of α-synuclein filaments from multiple system atrophy

M Schweighauser, Y Shi, A Tarutani, F Kametani… - Nature, 2020‏ - nature.com
Synucleinopathies, which include multiple system atrophy (MSA), Parkinson's disease,
Parkinson's disease with dementia and dementia with Lewy bodies (DLB), are human …

Protein misfolding, aggregation, and conformational strains in neurodegenerative diseases

C Soto, S Pritzkow - Nature neuroscience, 2018‏ - nature.com
A hallmark event in neurodegenerative diseases (NDs) is the misfolding, aggregation, and
accumulation of proteins, leading to cellular dysfunction, loss of synaptic connections, and …

Glutathione in brain disorders and aging

IY Iskusnykh, AA Zakharova, D Pathak - Molecules, 2022‏ - mdpi.com
Glutathione is a remarkably functional molecule with diverse features, which include being
an antioxidant, a regulator of DNA synthesis and repair, a protector of thiol groups in …

Ultrasensitive RT-QuIC assay with high sensitivity and specificity for Lewy body-associated synucleinopathies

M Rossi, N Candelise, S Baiardi, S Capellari… - Acta …, 2020‏ - Springer
The clinical diagnosis of synucleinopathies, including Parkinson's disease (PD), dementia
with Lewy bodies (DLB), and multiple system atrophy (MSA), is challenging, especially at an …

Meta‐analysis of gut dysbiosis in Parkinson's disease

H Nishiwaki, M Ito, T Ishida, T Hamaguchi… - Movement …, 2020‏ - Wiley Online Library
Background PD may begin with the intestinal accumulation of α‐synuclein fibrils, which can
be causally associated with gut dysbiosis. The variability of gut microbiota across countries …