Dystrophin Dp71: the smallest but multifunctional product of the Duchenne muscular dystrophy gene

R Tadayoni, A Rendon, LE Soria-Jasso… - Molecular …, 2012 - Springer
Dystrophin Dp71 is expressed in all tissues, with the exception of skeletal muscle, and is the
main Duchenne muscular dystrophy (DMD) gene product in brain. As full-length dystrophin …

Olfactory ensheathing cells: biology in neural development and regeneration

Z Su, C He - Progress in neurobiology, 2010 - Elsevier
Olfactory ensheathing cells (OECs) constitute a unique population of glia that accompany
and ensheath the primary olfactory axons. They are thought to be critical for spontaneous …

Neural map formation and sensory coding in the vomeronasal system

AC Brignall, JF Cloutier - Cellular and molecular life sciences, 2015 - Springer
Sensory systems enable us to encode a clear representation of our environment in the
nervous system by spatially organizing sensory stimuli being received. The organization of …

[HTML][HTML] Total absence of dystrophin expression exacerbates ectopic myofiber calcification and fibrosis and alters macrophage infiltration patterns

CNJ Young, MRF Gosselin, R Rumney… - The American Journal of …, 2020 - Elsevier
Duchenne muscular dystrophy (DMD) causes severe disability and death of young men
because of progressive muscle degeneration aggravated by sterile inflammation. DMD is …

Subcellular localization of dystrophin isoforms in cardiomyocytes and phenotypic analysis of dystrophin-deficient mice reveal cardiac myopathy is predominantly …

N Masubuchi, Y Shidoh, S Kondo, J Takatoh… - Experimental …, 2013 - jstage.jst.go.jp
Duchenne muscular dystrophy (DMD) is an X-linked recessive progressive muscle
degenerative disorder that causes dilated cardiomyopathy in the second decade of life in …

Olfactory ensheathing cells express α7 integrin to mediate their migration on laminin

NT Ingram, RR Khankan, PE Phelps - PLoS One, 2016 - journals.plos.org
The unique glia located in the olfactory system, called olfactory ensheathing cells (OECs),
are implicated as an attractive choice for transplantation therapy following spinal cord injury …

Dp71 gene disruption alters the composition of the dystrophin-associated protein complex and neuronal nitric oxide synthase expression in the hypothalamic …

R Benabdesselam, L Dorbani-Mamine… - Journal of …, 2012 - joe.bioscientifica.com
In the catfish Heteropneustes fossilis and Clarias batrachus, ovarian oestrogen-2-
hydroxylase (OE-2-H) activity increased significantly at 8 h after the injection of an ovulatory …

Reduction of abnormal behavioral response to brief restraint by information from other mice in dystrophin-deficient mdx mice

K Yamamoto, D Yamada, T Kabuta, A Takahashi… - Neuromuscular …, 2010 - Elsevier
We recently reported that dystrophin-deficient mdx mice exhibited a hypersensitive freezing
response to fearful events such as brief restraint. In the present study, we ethologically …

Diffusible, membrane-bound, and extracellular matrix factors from olfactory ensheathing cells have different effects on the self-renewing and differentiating properties …

L Cao, L Mu, Y Qiu, Z Su, Y Zhu, L Gao, Y Yuan, D Guo… - Brain research, 2010 - Elsevier
Transplantation of olfactory ensheathing cells (OECs) has been a promising strategy in
enhancing central nervous system (CNS) regeneration. However, little is known about the …

Deep phenoty** of the central nervous system in Duchenne muscular dystrophy

KE Maresh - 2022 - discovery.ucl.ac.uk
Duchenne muscular dystrophy (DMD) is an X-linked, life-limiting muscle-wasting disorder
caused by a loss of the protein dystrophin. Approximately half of DMD patients have …