Applied body-fluid analysis by wearable devices

N Brasier, J Wang, W Gao, JR Sempionatto, C Dincer… - Nature, 2024 - nature.com
Wearable sensors are a recent paradigm in healthcare, enabling continuous, decentralized,
and non-or minimally invasive monitoring of health and disease. Continuous measurements …

Standardised practices in the networked management of congenital hyperinsulinism: a UK national collaborative consensus

MG Shaikh, AK Lucas-Herald, A Dastamani… - Frontiers in …, 2023 - frontiersin.org
Congenital hyperinsulinism (CHI) is a condition characterised by severe and recurrent
hypoglycaemia in infants and young children caused by inappropriate insulin over …

[HTML][HTML] Treatment recommendations for glycogen storage disease type IB-associated neutropenia and neutrophil dysfunction with empagliflozin: Consensus from an …

SC Grünert, TGJ Derks, H Mundy, RN Dalton… - Molecular genetics and …, 2024 - Elsevier
Glycogen storage disease type Ib (GSD Ib, biallelic variants in SLC37A4) is a rare disorder
of glycogen metabolism complicated by neutropenia/neutrophil dysfunction. Since 2019, the …

Current understanding on pathogenesis and effective treatment of glycogen storage disease type Ib with empagliflozin: new insights coming from diabetes for its …

A Maiorana, F Tagliaferri, C Dionisi-Vici - Frontiers in Endocrinology, 2023 - frontiersin.org
Glycogen storage type Ib (GSDIb) is a rare inborn error of metabolism caused by glucose-6-
phosphate transporter (G6PT, SLC37A4) deficiency. G6PT defect results in excessive …

The behaviour change behind a successful pilot of hypoglycaemia reduction with HYPO-CHEAT

C Worth, PW Nutter, M Salomon-Estebanez… - Digital …, 2023 - journals.sagepub.com
Background Children with hypoglycaemia disorders, such as congenital hyperinsulinism
(CHI), are at constant risk of hypoglycaemia (low blood sugars) with the attendant risk of …

Continuous glucose monitoring in patients with inherited metabolic disorders at risk for Hypoglycemia and Nutritional implications

G Gugelmo, E Maines, F Boscari, L Lenzini… - Reviews in Endocrine …, 2024 - Springer
Abstract Managing Inherited Metabolic Disorders (IMDs) at risk for hypoglycemia, such as
Glycogen Storage Diseases (GSDs), Hereditary Fructose Metabolism Disorders (HFMDs) …

[HTML][HTML] Continuous glucose monitoring metrics in people with liver glycogen storage disease and idiopathic ketotic hypoglycemia: A single-center, retrospective …

RJ Overduin, A Venema, CMA Lubout… - Molecular Genetics and …, 2024 - Elsevier
Background Cohort data on continuous glucose monitoring (CGM) metrics are scarce for
liver glycogen storage diseases (GSDs) and idiopathic ketotic hypoglycemia (IKH). The aim …

Artificial intelligence in paediatric endocrinology: conflict or cooperation

P Dimitri, MO Savage - Journal of Pediatric Endocrinology and …, 2024 - degruyter.com
Artificial intelligence (AI) in medicine is transforming healthcare by automating system tasks,
assisting in diagnostics, predicting patient outcomes and personalising patient care …

Hypoglycaemia in adrenal insufficiency

SC Lee, ES Baranowski, R Sakremath… - Frontiers in …, 2023 - frontiersin.org
Adrenal insufficiency encompasses a group of congenital and acquired disorders that lead
to inadequate steroid production by the adrenal glands, mainly glucocorticoids …

The use of CGM to identify hypoglycemia and glycemic patterns in congenital hyperinsulinism

M Gariepy, N Yoosefi, C Silva, JP Chanoine… - Journal of Pediatric …, 2023 - degruyter.com
Objectives Unrecognized hypoglycemia, especially in the neonatal population, is a
significant cause of morbidity and poor neurologic outcomes. Children with congenital …