Disturbance of endoplasmic reticulum proteostasis in neurodegenerative diseases

C Hetz, B Mollereau - Nature Reviews Neuroscience, 2014 - nature.com
The unfolded protein response (UPR) is a homeostatic mechanism by which cells regulate
levels of misfolded proteins in the endoplasmic reticulum (ER). Although it is well …

The emerging role of zinc transporters in cellular homeostasis and cancer

E Bafaro, Y Liu, Y Xu, RE Dempski - Signal transduction and targeted …, 2017 - nature.com
Zinc is an essential micronutrient that plays a role in the structural or enzymatic functions of
many cellular proteins. Cellular zinc homeostasis involves the opposing action of two …

[HTML][HTML] Emerging roles of protein disulfide isomerase in cancer

E Lee - BMB reports, 2017 - ncbi.nlm.nih.gov
The protein disulfide isomerase (PDI) family is a group of multifunctional endoplasmic
reticulum (ER) enzymes that mediate the formation of disulfide bonds, catalyze the cysteine …

Protein disulfide isomerase in redox cell signaling and homeostasis

FRM Laurindo, LA Pescatore… - Free Radical Biology and …, 2012 - Elsevier
Thiol proteins may potentially act as redox signaling adaptor proteins, adjusting reactive
oxygen species intermediates to specific signals and redox signals to cell homeostasis. In …

Novel roles for protein disulphide isomerase in disease states: a double edged sword?

S Parakh, JD Atkin - Frontiers in cell and developmental biology, 2015 - frontiersin.org
Protein disulphide isomerase (PDI) is a multifunctional redox chaperone of the endoplasmic
reticulum (ER). Since it was first discovered 40 years ago the functions ascribed to PDI have …

The protein disulfide isomerase family: from proteostasis to pathogenesis

M Matsusaki, S Kanemura, M Kinoshita, YH Lee… - … et Biophysica Acta (BBA …, 2020 - Elsevier
In mammalian cells, nearly one-third of proteins are inserted into the endoplasmic reticulum
(ER), where they undergo oxidative folding and chaperoning assisted by approximately 20 …

Potential roles of the endoplasmic reticulum stress pathway in amyotrophic lateral sclerosis

YM Jeon, Y Kwon, S Lee, HJ Kim - Frontiers in Aging Neuroscience, 2023 - frontiersin.org
The endoplasmic reticulum (ER) is a major organelle involved in protein quality control and
cellular homeostasis. ER stress results from structural and functional dysfunction of the …

The function of the cellular prion protein in health and disease

JC Watts, MEC Bourkas, H Arshad - Acta neuropathologica, 2018 - Springer
The essential role of the cellular prion protein (PrP C) in prion disorders such as Creutzfeldt–
Jakob disease is well documented. Moreover, evidence is accumulating that PrP C may act …

[HTML][HTML] PDIA4: The basic characteristics, functions and its potential connection with cancer

Z Wang, H Zhang, Q Cheng - Biomedicine & Pharmacotherapy, 2020 - Elsevier
Disulfide bond formation is catalyzed by the protein disulfide Isomerases (PDI) family. This is
a critical step in protein folding which occurs within the endoplasmic reticulum. PDIA4, as a …

Evidence that bank vole PrP is a universal acceptor for prions

JC Watts, K Giles, S Patel, A Oehler… - PLoS …, 2014 - journals.plos.org
Bank voles are uniquely susceptible to a wide range of prion strains isolated from many
different species. To determine if this enhanced susceptibility to interspecies prion …