Cardiomyopathy in children: classification and diagnosis: a scientific statement from the American Heart Association

SE Lipshultz, YM Law, A Asante-Korang, ED Austin… - Circulation, 2019‏ - ahajournals.org
In this scientific statement from the American Heart Association, experts in the field of
cardiomyopathy (heart muscle disease) in children address 2 issues: the most current …

Left ventricular non-compaction cardiomyopathy

JA Towbin, A Lorts, JL Jefferies - The Lancet, 2015‏ - thelancet.com
Left ventricular non-compaction, the most recently classified form of cardiomyopathy, is
characterised by abnormal trabeculations in the left ventricle, most frequently at the apex. It …

Left ventricular noncompaction: a distinct genetic cardiomyopathy?

E Arbustini, V Favalli, N Narula, A Serio… - Journal of the American …, 2016‏ - jacc.org
Left ventricular noncompaction (LVNC) describes a ventricular wall anatomy characterized
by prominent left ventricular (LV) trabeculae, a thin compacted layer, and deep …

European heart rhythm association (EHRA)/heart rhythm society (HRS)/Asia pacific heart rhythm society (APHRS)/latin American heart rhythm society (LAHRS) expert …

AAM Wilde, C Semsarian, MF Márquez, AS Shamloo… - Europace, 2022‏ - academic.oup.com
Purpose Genetic testing has advanced significantly since the publication of the 2011
HRS/EHRA Expert Consensus Statement on the State of Genetic Testing for the …

Genetics of sudden cardiac death

CR Bezzina, N Lahrouchi, SG Priori - Circulation research, 2015‏ - ahajournals.org
Sudden cardiac death occurs in a broad spectrum of cardiac pathologies and is an important
cause of mortality in the general population. Genetic studies conducted during the past 20 …

Left ventricular noncompaction cardiomyopathy: cardiac, neuromuscular, and genetic factors

J Finsterer, C Stoellberger, JA Towbin - Nature Reviews Cardiology, 2017‏ - nature.com
Left ventricular hypertrabeculation (LVHT) or noncompaction is a myocardial abnormality of
unknown aetiology, frequently associated with monogenic disorders, particularly …

Molecular regulation of cardiomyocyte differentiation

SL Paige, K Plonowska, A Xu, SM Wu - Circulation research, 2015‏ - ahajournals.org
The heart is the first organ to form during embryonic development. Given the complex nature
of cardiac differentiation and morphogenesis, it is not surprising that some form of congenital …

Cardiomyopathies due to left ventricular noncompaction, mitochondrial and storage diseases, and inborn errors of metabolism

JA Towbin, JL Jefferies - Circulation research, 2017‏ - ahajournals.org
The normal function of the human myocardium requires the proper generation and utilization
of energy and relies on a series of complex metabolic processes to achieve this normal …

Genetic loci associated with heart rate variability and their effects on cardiac disease risk

IM Nolte, ML Munoz, V Tragante, AT Amare… - Nature …, 2017‏ - nature.com
Reduced cardiac vagal control reflected in low heart rate variability (HRV) is associated with
greater risks for cardiac morbidity and mortality. In two-stage meta-analyses of genome-wide …

Computational analysis of the human sinus node action potential: model development and effects of mutations

A Fabbri, M Fantini, R Wilders… - The Journal of …, 2017‏ - Wiley Online Library
Key points We constructed a comprehensive mathematical model of the spontaneous
electrical activity of a human sinoatrial node (SAN) pacemaker cell, starting from the recent …