Complement system part I–molecular mechanisms of activation and regulation

NS Merle, SE Church, V Fremeaux-Bacchi… - Frontiers in …, 2015 - frontiersin.org
Complement is a complex innate immune surveillance system, playing a key role in defense
against pathogens and in host homeostasis. The complement system is initiated by …

Complement activation, regulation, and molecular basis for complement‐related diseases

G Bajic, SE Degn, S Thiel, GR Andersen - The EMBO journal, 2015 - embopress.org
The complement system is an essential element of the innate immune response that
becomes activated upon recognition of molecular patterns associated with microorganisms …

Complement and its receptors: new insights into human disease

VM Holers - Annual review of immunology, 2014 - annualreviews.org
Although new activation and regulatory mechanisms are still being identified, the basic
architecture of the complement system has been known for decades. Two major roles of …

[HTML][HTML] Atypical hemolytic uremic syndrome

D Kavanagh, TH Goodship, A Richards - Seminars in nephrology, 2013 - Elsevier
Hemolytic uremic syndrome (HUS) is a triad of microangiopathic hemolytic anemia,
thrombocytopenia, and acute renal failure. The atypical form of HUS is a disease …

Atypical hemolytic uremic syndrome

C Loirat, V Frémeaux-Bacchi - Orphanet journal of rare diseases, 2011 - Springer
Hemolytic uremic syndrome (HUS) is defined by the triad of mechanical hemolytic anemia,
thrombocytopenia and renal impairment. Atypical HUS (aHUS) defines non Shiga-toxin …

Structural basis for sialic acid–mediated self-recognition by complement factor H

BS Blaum, JP Hannan, AP Herbert, D Kavanagh… - Nature chemical …, 2015 - nature.com
The serum protein complement factor H (FH) ensures downregulation of the complement
alternative pathway, a branch of innate immunity, upon interaction with specific glycans on …

Protection of host cells by complement regulators

CQ Schmidt, JD Lambris, D Ricklin - Immunological reviews, 2016 - Wiley Online Library
The complement cascade is an ancient immune‐surveillance system that not only provides
protection from pathogen invasion but has also evolved to participate in physiological …

Dimerization of complement factor H-related proteins modulates complement activation in vivo

E Goicoechea de Jorge, JJE Caesar… - Proceedings of the …, 2013 - National Acad Sciences
The complement system is a key component regulation influences susceptibility to age-
related macular degeneration, meningitis, and kidney disease. Variation includes genomic …

Complement factor H in host defense and immune evasion

R Parente, SJ Clark, A Inforzato, AJ Day - Cellular and Molecular Life …, 2017 - Springer
Complement is the major humoral component of the innate immune system. It recognizes
pathogen-and damage-associated molecular patterns, and initiates the immune response in …

Genetic variability shapes the alternative pathway complement activity and predisposition to complement‐related diseases

S Rodríguez de Córdoba - Immunological Reviews, 2023 - Wiley Online Library
The implementation of next‐generation sequencing technologies has provided a sharp
picture of the genetic variability in the components and regulators of the alternative pathway …