Laboratory approach to hemolytic anemia

M Jamwal, P Sharma, R Das - The Indian Journal of Pediatrics, 2020‏ - Springer
Hemolytic anemias are a group of disorders with varied clinical and molecular
heterogeneity. They are characterized by decreased levels of circulating erythrocytes in …

Multiple-ancestry genome-wide association study identifies 27 loci associated with measures of hemolysis following blood storage

GP Page, T Kanias, YJ Guo, MC Lanteri, X Zhang… - The Journal of Clinical …, 2021‏ - jci.org
Background The evolutionary pressure of endemic malaria and other erythrocytic pathogens
has shaped variation in genes encoding erythrocyte structural and functional proteins …

Biallelic hexokinase 1 (HK1) variants causative of non‐spherocytic haemolytic anaemia: A case series with emphasis on the HK1 promoter variant and literature …

EM Ukonmaanaho, S Dell'Anna… - British Journal of …, 2024‏ - Wiley Online Library
The hexokinase (HK) enzyme plays a key role in red blood cell energy production.
Hereditary non‐spherocytic haemolytic anaemia (HNSHA) caused by HK deficiency is a rare …

Spermatogenic cell-specific type 1 hexokinase (HK1S) is essential for capacitation-associated increase in tyrosine phosphorylation and male fertility in mice

Y Tian, X Chen, J Pu, Y Liang, W Li, X Xu, X Tan… - Plos …, 2024‏ - journals.plos.org
Hexokinase (HK) catalyzes the first irreversible rate-limiting step in glycolysis that converts
glucose to glucose-6-phosphate. HK1 is ubiquitously expressed in the brain, erythrocytes …

[HTML][HTML] Next-generation sequencing–based diagnosis of unexplained inherited hemolytic anemias reveals wide genetic and phenotypic heterogeneity

M Jamwal, A Aggarwal, A Palodhi, P Sharma… - The Journal of Molecular …, 2020‏ - Elsevier
Determination of the cause of inherited hemolysis is based on clinical and stepwise
conventional laboratory tests. Patients with obscure etiology require genetic diagnosis …

Sex-specific genetic modifiers identified susceptibility of cold stored red blood cells to osmotic hemolysis

F Fang, K Hazegh, AE Mast, DJ Triulzi, BR Spencer… - BMC genomics, 2022‏ - Springer
Background Genetic variants have been found to influence red blood cell (RBC)
susceptibility to hemolytic stress and affect transfusion outcomes and the severity of blood …

[HTML][HTML] A Novel Pathogenic Sense Variant in Exon 7 of the HK1 Gene in a Patient with Hexokinase Deficiency and Gilbert Syndrome

M Bartnik, W Pawlik, B Burzyńska, K Wasilewski… - Genes, 2024‏ - mdpi.com
Background: Hexokinase (HK) deficiency is a rare autosomal recessively inherited disease
manifested by chronic nonspherocytic hemolytic anemia. Most patients present with a mild to …

Expanding the neurodevelopmental phenotype associated with HK1 de novo heterozygous missense variants

RL Poole, M Badonyi, A Cozens, N Foulds… - European journal of …, 2023‏ - Elsevier
Neurodevelopmental disorder with visual defects and brain anomalies (NEDVIBA) is a
recently described genetic condition caused by de novo missense HK1 variants. Phenotypic …

Cross-cohort analysis of expression and splicing quantitative trait loci in TOPMed

P Orchard, TW Blackwell, L Kachuri, PJ Castaldi… - medRxiv, 2025‏ - medrxiv.org
Most genetic variants associated with complex traits and diseases occur in non-coding
genomic regions and are hypothesized to regulate gene expression. To understand the …

A de novo hexokinase 1 (HK1) variant presenting as Boucher–Neuhäuser syndrome

RH Peretz, WM Zein, RB Hufnagel, C Ku… - American Journal of …, 2023‏ - Wiley Online Library
Boucher–Neuhäuser syndrome (BNHS) is characterized by chorioretinal dystrophy,
hypogonadotropic hypogonadism, and cerebellar dysfunction and atrophy. The disorder has …