Inhibitors of dermatan sulfate epimerase 1 decreased accumulation of glycosaminoglycans in mucopolysaccharidosis type I fibroblasts

M Maccarana, B Li, H Li, J Fang, M Yu, J Li - Glycobiology, 2024 - academic.oup.com
Genetic deficiency of alpha-L-iduronidase causes mucopolysaccharidosis type I (MPS-I)
disease, due to accumulation of glycosaminoglycans (GAGs) including …

Inhibition of iduronic acid biosynthesis by ebselen reduces glycosaminoglycan accumulation in mucopolysaccharidosis type I fibroblasts

M Maccarana, E Tykesson, EM Pera, N Gouignard… - …, 2021 - academic.oup.com
Abstract Mucopolysaccharidosis type I (MPS-I) is a rare lysosomal storage disorder caused
by deficiency of the enzyme alpha-L-iduronidase, which removes iduronic acid in both …

[HTML][HTML] Computational modeling of the molecular basis for the calcium-dependence of the mannuronan C-5 epimerase AvAlgE6 from Azotobacter vinelandii

M Gaardløs, A Lervik, SA Samsonov - Computational and Structural …, 2023 - Elsevier
The mannuronan C-5 epimerases catalyze epimerization of β-d-mannuronic acid to α-l-
guluronic acid in alginate polymers. The seven extracellular Azotobacter vinelandii …

Cheetah-MS: a web server to model protein complexes using tandem cross-linking mass spectrometry data

H Khakzad, L Happonen, J Malmström… - …, 2021 - academic.oup.com
Protein–protein interactions (PPIs) are central in many biological processes but difficult to
characterize, especially in complex, unfractionated samples. Chemical cross-linking …

[HTML][HTML] Molecular docking analysis of a dermatan sulfate tetra-saccharide to human alpha-L-iduronidase

DP Durán-Gutiérrez, M López-Hidalgo… - …, 2023 - ncbi.nlm.nih.gov
Human alpha-L-iduronidase (IDUA) is a 653 amino acid protein involved in the sequential
degradation of glycos-amino-glycans (GAG), heparan sulfate (HS), and dermatan sulfate …

Engineering the extracellular matrix to model diseases and orchestrate regeneration

Z Söderlund - 2023 - portal.research.lu.se
The extracellular matrix is not only a scaffold to which cells attach, but it is also a matrix that
communicates cell signals. Because of the interplay between cells and the extracellular …