Meningiomas are the most common primary intracranial tumors. The majority of
meningiomas are benign, but they can present different grades of dedifferentiation from …

Neurofibromatosis type 2 is an autosomal-dominant multiple neoplasia syndrome that
results from mutations in the NF2 tumour suppressor gene located on chromosome 22q. It …

Dominantly inherited tumor-prone syndromes are a significant health burden, but disease-
related morbidity can be reduced and life expectancy increased by a GR type approach …

The neurofibromatoses are a heterogeneous group of hereditary cancer syndromes that
lead to tumors of the central and peripheral nervous systems, as well as other organ …

Abstract Neurofibromatosis type 2 (NF2) is a tumour-prone disorder characterised by the
development of multiple schwannomas and meningiomas. Prevalence (initially estimated at …

Neurofibromatosis type II (NF2) is a tumor predisposition syndrome characterized by the
development of distinctive nervous system lesions. NF2 results from loss-of-function …

Objective: To determine the incidence of vestibular schwannoma (VS) in sporadic,
neurofibromatosis type 2 (NF2) germ-line and mosaic form in a 10-year period. Study …

The neurofibromatoses are a diverse group of genetic conditions that share a predisposition
to the development of tumors of the nerve sheath. Schwannomatosis is a recently …

Abstract Neurofibromatosis type 1 (NF1), neurofibromatosis type 2 (NF2), and
schwannomatosis (SWN) are three clinically distinct tumor predisposition syndromes with a …

Introduction: Vestibular schwannomas (VS) account for approximately 85% of tumors in the
cerebello-pontine angle, with a lifetime incidence of approximately 1 in 1000. Most are …