Pemphigus

M Kasperkiewicz, CT Ellebrecht, H Takahashi… - Nature reviews Disease …, 2017 - nature.com
Pemphigus is a group of IgG-mediated autoimmune diseases of stratified squamous
epithelia, such as the skin and oral mucosa, in which acantholysis (the loss of cell adhesion) …

Update on the use of immunoglobulin in human disease: a review of evidence

EE Perez, JS Orange, F Bonilla, J Chinen… - Journal of Allergy and …, 2017 - Elsevier
Human immunoglobulin preparations for intravenous or subcutaneous administration are
the cornerstone of treatment in patients with primary immunodeficiency diseases affecting …

Updated S2K guidelines on the management of pemphigus vulgaris and foliaceus initiated by the european academy of dermatology and venereology (EADV)

P Joly, B Horvath, Α Patsatsi, S Uzun… - Journal of the …, 2020 - Wiley Online Library
Background Pemphigus encompasses a group of life‐threatening autoimmune bullous
diseases characterized by blisters and erosions of the mucous membranes and skin. Before …

Pemphigus: current and future therapeutic strategies

D Didona, R Maglie, R Eming, M Hertl - Frontiers in immunology, 2019 - frontiersin.org
Pemphigus encompasses a heterogeneous group of autoimmune blistering diseases, which
affect both mucous membranes and the skin. The disease usually runs a chronic-relapsing …

[HTML][HTML] Pemphigus vulgaris

AM Porro, CA Seque, MCC Ferreira - Anais brasileiros de …, 2019 - SciELO Brasil
Pemphigus vulgaris is a chronic autoimmune bullous dermatosis that results from the
production of autoantibodies against desmogleins 1 and 3. It is the most frequent and most …

Mechanisms of disease: pemphigus and bullous pemphigoid

CM Hammers, JR Stanley - Annual Review of Pathology …, 2016 - annualreviews.org
Pemphigus and bullous pemphigoid are autoantibody-mediated blistering skin diseases. In
pemphigus, keratinocytes in epidermis and mucous membranes lose cell-cell adhesion, and …

British Association of Dermatologists' guidelines for the management of pemphigus vulgaris 2017

KE Harman, D Brown, LS Exton… - British Journal of …, 2017 - academic.oup.com
British Association of Dermatologists’ guidelines for the management of pemphigus vulgaris
2017 | British Journal of Dermatology | Oxford Academic Skip to Main Content Advertisement …

Pemphigus. S2 Guideline for diagnosis and treatment–guided by the European Dermatology Forum (EDF) in cooperation with the European Academy of Dermatology …

M Hertl, H Jedlickova, S Karpati… - Journal of the …, 2015 - Wiley Online Library
Background Pemphigus encompasses a group of life‐threatening autoimmune bullous
diseases characterized by blisters and erosions of the mucous membranes and skin. Before …

Pemphigus

E Schmidt, M Kasperkiewicz, P Joly - The Lancet, 2019 - thelancet.com
Pemphigus consists of a group of rare and severe autoimmune blistering diseases mediated
by pathogenic autoantibodies mainly directed against two desmosomal adhesion proteins …

Treatment of pemphigus vulgaris and foliaceus with efgartigimod, a neonatal Fc receptor inhibitor: a phase II multicentre, open‐label feasibility trial

M Goebeler, Z Bata‐Csörgő… - British Journal of …, 2022 - academic.oup.com
Background Pemphigus vulgaris and pemphigus foliaceus are potentially life‐threatening
autoimmune disorders triggered by IgG autoantibodies against mucosal and epidermal …