Medulloblastoma

PA Northcott, GW Robinson, CP Kratz… - Nature reviews Disease …, 2019 - nature.com
Medulloblastoma (MB) comprises a biologically heterogeneous group of embryonal tumours
of the cerebellum. Four subgroups of MB have been described (WNT, sonic hedgehog …

Retinitis pigmentosa: progress in molecular pathology and biotherapeutical strategies

W Liu, S Liu, P Li, K Yao - International Journal of Molecular Sciences, 2022 - mdpi.com
Retinitis pigmentosa (RP) is genetically heterogeneous retinopathy caused by
photoreceptor cell death and retinal pigment epithelial atrophy that eventually results in …

Unified rhombic lip origins of group 3 and group 4 medulloblastoma

KS Smith, L Bihannic, BL Gudenas, P Haldipur, R Tao… - Nature, 2022 - nature.com
Medulloblastoma, a malignant childhood cerebellar tumour, segregates molecularly into
biologically distinct subgroups, suggesting that a personalized approach to therapy would …

Circular extrachromosomal DNA promotes tumor heterogeneity in high-risk medulloblastoma

OS Chapman, J Luebeck, S Sridhar, ITL Wong, D Dixit… - Nature …, 2023 - nature.com
Circular extrachromosomal DNA (ecDNA) in patient tumors is an important driver of
oncogenic gene expression, evolution of drug resistance and poor patient outcomes …

Modeling medulloblastoma in vivo and with human cerebellar organoids

C Ballabio, M Anderle, M Gianesello, C Lago… - Nature …, 2020 - nature.com
Medulloblastoma (MB) is the most common malignant brain tumor in children and among
the subtypes, Group 3 MB has the worst outcome. Here, we perform an in vivo, patient …

Neoplastic and immune single-cell transcriptomics define subgroup-specific intra-tumoral heterogeneity of childhood medulloblastoma

KA Riemondy, S Venkataraman, N Willard… - Neuro …, 2022 - academic.oup.com
Background Medulloblastoma (MB) is a heterogeneous disease in which neoplastic cells
and associated immune cells contribute to disease progression. We aimed to determine the …

Medulloblastoma group 3 and 4 tumors comprise a clinically and biologically significant expression continuum reflecting human cerebellar development

D Williamson, EC Schwalbe, D Hicks, KA Aldinger… - Cell reports, 2022 - cell.com
Medulloblastoma is currently subclassified into distinct DNA methylation
subgroups/subtypes with particular clinico-molecular features. Using RNA sequencing (RNA …

Chromatin landscapes reveal developmentally encoded transcriptional states that define human glioblastoma

SC Mack, I Singh, X Wang, R Hirsch, Q Wu… - Journal of Experimental …, 2019 - rupress.org
Glioblastoma is an incurable brain cancer characterized by high genetic and pathological
heterogeneity. Here, we mapped active chromatin landscapes with gene expression, whole …

Loss of phosphatase CTDNEP1 potentiates aggressive medulloblastoma by triggering MYC amplification and genomic instability

Z Luo, D **n, Y Liao, K Berry, S Ogurek, F Zhang… - Nature …, 2023 - nature.com
MYC-driven medulloblastomas are highly aggressive childhood brain tumors, however, the
molecular and genetic events triggering MYC amplification and malignant transformation …

Core transcriptional regulatory circuitries in cancer

Y Chen, L Xu, RYT Lin, M Müschen, HP Koeffler - Oncogene, 2020 - nature.com
Transcription factors (TFs) coordinate the on-and-off states of gene expression typically in a
combinatorial fashion. Studies from embryonic stem cells and other cell types have revealed …