Congenital hearing loss

AMH Korver, RJH Smith, G Van Camp… - Nature reviews Disease …, 2017 - nature.com
Congenital hearing loss (hearing loss that is present at birth) is one of the most prevalent
chronic conditions in children. In the majority of developed countries, neonatal hearing …

Massively parallel sequencing for genetic diagnosis of hearing loss: the new standard of care

AE Shearer, RJH Smith - Otolaryngology–Head and Neck …, 2015 - journals.sagepub.com
Objective To evaluate the use of new genetic sequencing techniques for comprehensive
genetic testing for hearing loss. Data Sources Articles were identified from PubMed and …

Comprehensive genetic testing in the clinical evaluation of 1119 patients with hearing loss

CM Sloan-Heggen, AO Bierer, AE Shearer, DL Kolbe… - Human genetics, 2016 - Springer
Hearing loss is the most common sensory deficit in humans, affecting 1 in 500 newborns.
Due to its genetic heterogeneity, comprehensive diagnostic testing has not previously been …

Genomic landscape and mutational signatures of deafness-associated genes

H Azaiez, KT Booth, SS Ephraim, B Crone… - The American Journal of …, 2018 - cell.com
The classification of genetic variants represents a major challenge in the post-genome era
by virtue of their extraordinary number and the complexities associated with ascribing a …

[HTML][HTML] Genomic analyses of hair from Ludwig van Beethoven

TJA Begg, A Schmidt, A Kocher, MHD Larmuseau… - Current Biology, 2023 - cell.com
Summary Ludwig van Beethoven (1770–1827) remains among the most influential and
popular classical music composers. Health problems significantly impacted his career as a …

[HTML][HTML] Hereditary hearing loss and deafness overview

AE Shearer, MS Hildebrand, RJH Smith - 2017 - europepmc.org
Hereditary Hearing Loss and Deafness Overview - Abstract - Europe PMC Sign in | Create an
account https://orcid.org Europe PMC Menu About Tools Developers Help Contact us …

Detection of clinically relevant copy-number variants by exome sequencing in a large cohort of genetic disorders

R Pfundt, M Del Rosario, LELM Vissers, MP Kwint… - Genetics in …, 2017 - nature.com
Purpose: Copy-number variation is a common source of genomic variation and an important
genetic cause of disease. Microarray-based analysis of copy-number variants (CNVs) has …

Genomic sequencing for newborn screening: results of the NC NEXUS project

TS Roman, SB Crowley, MI Roche… - The American Journal of …, 2020 - cell.com
Newborn screening (NBS) was established as a public health program in the 1960s and is
crucial for facilitating detection of certain medical conditions in which early intervention can …

Dosage sensitivity is a major determinant of human copy number variant pathogenicity

AM Rice, A McLysaght - Nature communications, 2017 - nature.com
Human copy number variants (CNVs) account for genome variation an order of magnitude
larger than single-nucleotide polymorphisms. Although much of this variation has no …

[HTML][HTML] Optical genome map** and revisiting short-read genome sequencing data reveal previously overlooked structural variants disrupting retinal disease …

SE de Bruijn, K Rodenburg, J Corominas… - Genetics in …, 2023 - Elsevier
Abstract Purpose Structural variants (SVs) play an important role in inherited retinal
diseases (IRD). Although the identification of SVs significantly improved upon the availability …