The biological function of the cellular prion protein: an update

MA Wulf, A Senatore, A Aguzzi - BMC biology, 2017 - Springer
The misfolding of the cellular prion protein (PrP C) causes fatal neurodegenerative
diseases. Yet PrP C is highly conserved in mammals, suggesting that it exerts beneficial …

Physiology of the prion protein

R Linden, VR Martins, MAM Prado… - Physiological …, 2008 - journals.physiology.org
Prion diseases are transmissible spongiform encephalopathies (TSEs), attributed to
conformational conversion of the cellular prion protein (PrPC) into an abnormal conformer …

Autism-specific maternal autoantibodies recognize critical proteins in develo** brain

D Braunschweig, P Krakowiak, P Duncanson… - Translational …, 2013 - nature.com
Autism spectrum disorders (ASDs) are neurodevelopmental in origin, affecting an estimated
1 in 88 children in the United States. We previously described ASD-specific maternal …

Anti-brain antibodies are associated with more severe cognitive and behavioral profiles in Italian children with Autism Spectrum Disorder

IS Piras, L Haapanen, V Napolioni, R Sacco… - Brain, behavior, and …, 2014 - Elsevier
Circulating 45 and 62 kDa antibodies targeting the cerebellum were previously associated
with Autism Spectrum Disorder (ASD), lower adaptive/cognitive function and aberrant …

Role of α7 nicotinic acetylcholine receptor in calcium signaling induced by prion protein interaction with stress-inducible protein 1

FH Beraldo, CP Arantes, TG Santos… - Journal of Biological …, 2010 - ASBMB
The prion protein (PrP C) is a conserved glycosylphosphatidylinositol-anchored cell surface
protein expressed by neurons and other cells. Stress-inducible protein 1 (STI1) binds PrP C …

Prion protein interaction with stress-inducible protein 1 enhances neuronal protein synthesis via mTOR

M Roffé, FH Beraldo, R Bester… - Proceedings of the …, 2010 - National Acad Sciences
Transmissible spongiform encephalopathies are fatal neurodegenerative diseases caused
by the conversion of prion protein (PrPC) into an infectious isoform (PrPSc). How this event …

Maternal autoantibody related autism: mechanisms and pathways

KL Jones, J Van de Water - Molecular psychiatry, 2019 - nature.com
It has been estimated that autism spectrum disorder (ASD) now affects 1 in 59 children in the
United States. Although the cause (s) of ASD remain largely unknown, it is becoming …

Increased expression of stress inducible protein 1 in glioma-associated microglia/macrophages

ACC da Fonseca, H Wang, H Fan, X Chen… - Journal of …, 2014 - Elsevier
Factors released by glioma-associated microglia/macrophages (GAMs) play an important
role in the growth and infiltration of tumors. We have previously demonstrated that the co …

PRNP/prion protein regulates the secretion of exosomes modulating CAV1/caveolin-1-suppressed autophagy

MVS Dias, BL Teixeira, BR Rodrigues… - Autophagy, 2016 - Taylor & Francis
Prion protein modulates many cellular functions including the secretion of trophic factors by
astrocytes. Some of these factors are found in exosomes, which are formed within …

Dissecting the copper bioinorganic chemistry of the functional and pathological roles of the prion protein: Relevance in Alzheimer's disease and cancer

Y Posadas, VE López-Guerrero, J Segovia… - Current opinion in …, 2022 - Elsevier
The cellular prion protein (PrP C) is a metal-binding biomolecule that can interact with
different protein partners involved in pivotal physiological processes, such as neurogenesis …