Ancestry-inclusive dog genomics challenges popular breed stereotypes

K Morrill, J Hekman, X Li, J McClure, B Logan… - Science, 2022 - science.org
Behavioral genetics in dogs has focused on modern breeds, which are isolated subgroups
with distinctive physical and, purportedly, behavioral characteristics. We interrogated breed …

Update on recommendations for cancer screening and surveillance in children with genomic instability disorders

Y Nakano, RP Kuiper, KE Nichols… - Clinical Cancer …, 2024 - aacrjournals.org
Genomic instability disorders are characterized by DNA or chromosomal instability, resulting
in various clinical manifestations, including developmental anomalies, immunodeficiency …

Premature aging disorders: A clinical and genetic compendium

F Schnabel, U Kornak, B Wollnik - Clinical Genetics, 2021 - Wiley Online Library
Progeroid disorders make up a heterogeneous group of very rare hereditary diseases
characterized by clinical signs that often mimic physiological aging in a premature manner …

[HTML][HTML] The role of Anaphase Promoting Complex activation, inhibition and substrates in cancer development and progression

C VanGenderen, TAA Harkness, TG Arnason - Aging (Albany NY), 2020 - ncbi.nlm.nih.gov
Abstract The Anaphase Promoting Complex (APC), a multi-subunit ubiquitin ligase,
facilitates mitotic and G1 progression, and is now recognized to play a role in maintaining …

Congenital diseases of DNA replication: clinical phenotypes and molecular mechanisms

M Schmit, AK Bielinsky - International journal of molecular sciences, 2021 - mdpi.com
Deoxyribonucleic acid (DNA) replication can be divided into three major steps: initiation,
elongation and termination. Each time a human cell divides, these steps must be …

[HTML][HTML] Biallelic variants in CRIPT cause a Rothmund-Thomson-like syndrome with increased cellular senescence

L Averdunk, MA Huetzen, D Moreno-Andrés, R Kalb… - Genetics in …, 2023 - Elsevier
Abstract Purpose Rothmund-Thomson syndrome (RTS) is characterized by poikiloderma,
sparse hair, small stature, skeletal defects, cancer, and cataracts, resembling features of …

Role and regulation of the RECQL4 family during genomic integrity maintenance

TT Luong, KA Bernstein - Genes, 2021 - mdpi.com
RECQL4 is a member of the evolutionarily conserved RecQ family of 3'to 5'DNA helicases.
RECQL4 is critical for maintaining genomic stability through its functions in DNA repair …

[HTML][HTML] Patient-derived iPSCs link elevated mitochondrial respiratory complex I function to osteosarcoma in Rothmund-Thomson syndrome

BE Jewell, A Xu, D Zhu, MF Huang, L Lu, M Liu… - PLoS …, 2021 - journals.plos.org
Rothmund-Thomson syndrome (RTS) is an autosomal recessive genetic disorder
characterized by poikiloderma, small stature, skeletal anomalies, sparse brows/lashes …

Genome-wide association screening determines peripheral players in male fertility maintenance

T Greither, HM Behre, H Herlyn - International Journal of Molecular …, 2022 - mdpi.com
Deciphering the functional relationships of genes resulting from genome-wide screens for
polymorphisms that are associated with phenotypic variations can be challenging. However …

[HTML][HTML] Rothmund-thomson syndrome

LL Wang, SE Plon - 2020 - europepmc.org
Rothmund-Thomson syndrome (RTS) is characterized by a rash that progresses to
poikiloderma; sparse hair, eyelashes, and/or eyebrows; small size; skeletal and dental …