Transthyretin: Its function and amyloid formation

M Ueda - Neurochemistry international, 2022‏ - Elsevier
Transthyretin (TTR), which is one of the major amyloidogenic proteins in systemic
amyloidosis, forms extracellular amyloid deposits in the systemic organs such as nerves …

The role of proteolysis in amyloidosis

L Acquasaliente, V De Filippis - International Journal of Molecular …, 2022‏ - mdpi.com
Amyloidoses are a group of diseases associated with deposits of amyloid fibrils in different
tissues. So far, 36 different types of amyloidosis are known, each due to the misfolding and …

From haemadin to haemanorm: Synthesis and characterization of full‐length haemadin from the leech Haemadipsa sylvestris and of a novel bivalent, highly potent …

L Acquasaliente, A Pierangelini, A Pagotto… - Protein …, 2023‏ - Wiley Online Library
Hirudin from Hirudo medicinalis is a bivalent α‐Thrombin (αT) inhibitor, targeting the enzyme
active site and exosite‐I, and is currently used in anticoagulant therapy along with its …

Exogenous human α-Synuclein acts in vitro as a mild platelet antiaggregant inhibiting α-thrombin-induced platelet activation

L Acquasaliente, G Pontarollo, CM Radu, D Peterle… - Scientific Reports, 2022‏ - nature.com
Abstract α-Synuclein (αSyn) is a small disordered protein, highly conserved in vertebrates
and involved in the pathogenesis of Parkinson's disease (PD). Indeed, αSyn amyloid …

Role of microbial secreted proteins in gut microbiota-host interactions

B Vidal-Veuthey, D González… - Frontiers in Cellular and …, 2022‏ - frontiersin.org
The mammalian gut microbiota comprises a variety of commensals including potential
probiotics and pathobionts, influencing the host itself. Members of the microbiota can …

Degradation versus fibrillogenesis, two alternative pathways modulated by seeds and glycosaminoglycans

G Verona, S Raimondi, D Canetti… - Protein …, 2024‏ - Wiley Online Library
The mechanism that converts native human transthyretin into amyloid fibrils in vivo is still a
debated and controversial issue. Commonly, non‐physiological conditions of pH …

Transthyretin misfolding, a fatal structural pathogenesis mechanism

JB Si, B Kim, JH Kim - International journal of molecular sciences, 2021‏ - mdpi.com
Transthyretin (TTR) is an essential transporter of a thyroid hormone and a holo-retinol
binding protein, found abundantly in human plasma and cerebrospinal fluid. In addition, this …

[HTML][HTML] Current and emerging therapies for hereditary transthyretin amyloidosis: strides towards a brighter future

L Obici, R Mussinelli - Neurotherapeutics, 2021‏ - Elsevier
The past few years have witnessed an unprecedented acceleration in the clinical
development of novel therapeutic options for hereditary transthyretin amyloidosis. Recently …

Association between rat decompression sickness resistance, transthyretin single nucleotide polymorphism, and expression: A pilot study

J Orsat, A Guernec, C Le Maréchal… - Physiological …, 2024‏ - Wiley Online Library
Decompression sickness (DCS) is a systemic syndrome that can occur after an
environmental pressure reduction. Previously, we showed that the plasmatic tetrameric form …

Emerging therapeutic avenues in cardiac amyloidosis

V Golatkar, LK Bhatt - European Journal of Pharmacology, 2023‏ - Elsevier
Cardiac Amyloidosis (CA) is a toxic infiltrative cardiomyopathy occurred by the deposition of
the amyloid fibres in the extracellular matrix of the myocardium. This results in severe clinical …