Idiopathic pulmonary fibrosis (IPF) is a progressive lung disease with a poor prognosis.
Lung transplantation is the only intervention shown to increase life expectancy for patients …

Pleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique
clinical, radiological, and pathological characteristics. Designated a rare idiopathic …

Background: This American Thoracic Society, European Respiratory Society, Japanese
Respiratory Society, and Asociación Latinoamericana de Tórax guideline updates prior …

Background Physicians have few opportunities to perform surgical lung biopsy (SLB) to
diagnose idiopathic pleuroparenchymal fibroelastosis (IPPFE). Therefore, diagnostic criteria …

Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine
Pleuroparenchymal fibroelastosis : Current Opinion in Pulmonary Medicine Log in or …

The world of rare interstitial lung diseases (ILDs) is diverse and complex. Diagnosis and
therapy usually pose challenges. This review describes a selection of rare and ultrarare …

BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) has been described in
hypersensitivity pneumonitis (HP) yet its functional implications are unclear. Combined …

Background Pleuroparenchymal fibroelastosis (PPFE) is a rare subset of idiopathic
interstitial pneumonias. No large-scale clinical studies of PPFE have been published. The …

Pleuroparenchymal fibroelastosis (PPFE) is characterized by fibrosis involving the pleura
and subpleural lung parenchyma, predominantly in the upper lobes. As PPFE appears to …

Background Clinical course of pleuroparenchymal fibroelastosis (PPFE) shows
considerable variation among patients, but there is no established prognostic prediction …