The future of cystic fibrosis care: a global perspective

SC Bell, MA Mall, H Gutierrez, M Macek… - The Lancet …, 2020 - thelancet.com
Executive summary The past six decades have seen remarkable improvements in health
outcomes for people with cystic fibrosis, which was once a fatal disease of infants and young …

Cystic fibrosis lung environment and Pseudomonas aeruginosa infection

AY Bhagirath, Y Li, D Somayajula, M Dadashi… - BMC pulmonary …, 2016 - Springer
Background The airways of patients with cystic fibrosis (CF) are highly complex, subject to
various environmental conditions as well as a distinct microbiota. Pseudomonas aeruginosa …

New pharmacological approaches for cystic fibrosis: promises, progress, pitfalls

SC Bell, K De Boeck, MD Amaral - Pharmacology & therapeutics, 2015 - Elsevier
With the discovery of the CFTR gene in 1989, the search for therapies to improve the basic
defects of cystic fibrosis (CF) commenced. Pharmacological manipulation provides the …

Age trends in 30 day hospital readmissions: US national retrospective analysis

JG Berry, JC Gay, KJ Maddox, EA Coleman… - bmj, 2018 - bmj.com
Objective To assess trends in and risk factors for readmission to hospital across the age
continuum. Design Retrospective analysis. Setting and participants 31 729 762 index …

[HTML][HTML] Treatment complexity in cystic fibrosis: trends over time and associations with site-specific outcomes

GS Sawicki, CL Ren, MW Konstan, SJ Millar… - Journal of Cystic …, 2013 - Elsevier
Background Patients with cystic fibrosis (CF) have increasing treatment complexity and high
treatment burden. We describe trends in treatment complexity and evaluate its relationship …

Motivating adherence among adolescents with cystic fibrosis: youth and parent perspectives

GS Sawicki, KS Heller, N Demars… - Pediatric …, 2015 - Wiley Online Library
As advances in the care of individuals with cystic fibrosis (CF) have resulted in improved
survival, therapeutic regimens for treatment of CF have become increasingly complex. This …

Pseudomonas aeruginosa infection in patients with cystic fibrosis: scientific evidence regarding clinical impact, diagnosis, and treatment

LVRF Silva Filho, FA Ferreira, FJC Reis… - Jornal Brasileiro de …, 2013 - SciELO Brasil
Evidence-based techniques have been increasingly used in the creation of clinical
guidelines and the development of recommendations for medical practice. The use of levels …

Associations between micronutrient intakes and gut microbiota in a group of adults with cystic fibrosis

L Li, L Krause, S Somerset - Clinical nutrition, 2017 - Elsevier
Background Cystic fibrosis (CF) involves chronic inflammation and oxidative stress affecting
mainly the respiratory and digestive systems. Survival rates for CF have improved with …

Answering the call to address cystic fibrosis treatment burden in the era of highly effective CFTR modulator therapy

AH Gifford, N Mayer-Hamblett, K Pearson… - Journal of Cystic …, 2020 - Elsevier
Background We recognize an unprecedented opportunity to study the effects of withdrawing
one or more chronic treatments in people with CF (PwCF) who benefit greatly from CFTR …

Entering the era of highly effective modulator therapies

K Dave, R Dobra, S Scott, C Saunders… - Pediatric …, 2021 - Wiley Online Library
Since the discovery of the gene responsible for cystic fibrosis (CF) in 1989, hopes have
been pinned on a future with novel therapies tackling the basis of the disease rather than its …