[HTML][HTML] Quality control of the mitochondrion

MYW Ng, T Wai, A Simonsen - Developmental cell, 2021 - cell.com
Mitochondria are essential organelles that execute and coordinate various metabolic
processes in the cell. Mitochondrial dysfunction severely affects cell fitness and contributes …

Lipids of mitochondria

SE Horvath, G Daum - Progress in lipid research, 2013 - Elsevier
A unique organelle for studying membrane biochemistry is the mitochondrion whose
functionality depends on a coordinated supply of proteins and lipids. Mitochondria are …

NAD+ repletion improves mitochondrial and stem cell function and enhances life span in mice

H Zhang, D Ryu, Y Wu, K Gariani, X Wang, P Luan… - Science, 2016 - science.org
Adult stem cells (SCs) are essential for tissue maintenance and regeneration yet are
susceptible to senescence during aging. We demonstrate the importance of the amount of …

PINK1 import regulation; a fine system to convey mitochondrial stress to the cytosol

S Sekine, RJ Youle - BMC biology, 2018 - Springer
Insights from inherited forms of parkinsonism suggest that insufficient mitophagy may be one
etiology of the disease. PINK1/Parkin-dependent mitophagy, which helps maintain a healthy …

The mitochondrial fusion protein OPA1 is dispensable in the liver and its absence induces mitohormesis to protect liver from drug-induced injury

H Lee, TJ Lee, CA Galloway, W Zhi, W **ao… - Nature …, 2023 - nature.com
Mitochondria are critical for metabolic homeostasis of the liver, and their dysfunction is a
major cause of liver diseases. Optic atrophy 1 (OPA1) is a mitochondrial fusion protein with a …

Making heads or tails of phospholipids in mitochondria

C Osman, DR Voelker, T Langer - Journal of Cell Biology, 2011 - rupress.org
Mitochondria are dynamic organelles whose functional integrity requires a coordinated
supply of proteins and phospholipids. Defined functions of specific phospholipids, like the …

CARL lncRNA inhibits anoxia-induced mitochondrial fission and apoptosis in cardiomyocytes by impairing miR-539-dependent PHB2 downregulation

K Wang, BO Long, LY Zhou, F Liu, QY Zhou… - Nature …, 2014 - nature.com
Abnormal mitochondrial fission participates in the pathogenesis of many diseases. Long non-
coding RNAs (lncRNAs) are emerging as new players in gene regulation, but how lncRNAs …

[HTML][HTML] Cardiolipin and mitochondrial cristae organization

N Ikon, RO Ryan - Biochimica et Biophysica Acta (BBA)-Biomembranes, 2017 - Elsevier
A fundamental question in cell biology, under investigation for over six decades, is the
structural organization of mitochondrial cristae. Long known to harbor electron transport …

[HTML][HTML] Mitochondria: the next (neurode) generation

EA Schon, S Przedborski - Neuron, 2011 - cell.com
Adult-onset neurodegenerative disorders are disabling and often fatal diseases of the
nervous system whose underlying mechanisms of cell death remain unknown. Defects in …

[HTML][HTML] C9orf72 regulates energy homeostasis by stabilizing mitochondrial complex I assembly

T Wang, H Liu, K Itoh, S Oh, L Zhao, D Murata… - Cell metabolism, 2021 - cell.com
The haploinsufficiency of C9orf72 is implicated in the most common forms of amyotrophic
lateral sclerosis (ALS) and frontotemporal dementia (FTD), but the full spectrum of C9orf72 …