Clinical practice guidelines from the cystic fibrosis foundation for preschoolers with cystic fibrosis

T Lahiri, SE Hempstead, C Brady, CL Cannon… - …, 2016‏ - publications.aap.org
Clinical Practice Guidelines From the Cystic Fibrosis Foundation for Preschoolers With
Cystic Fibrosis | Pediatrics | American Academy of Pediatrics Skip to Main Content …

Current state of the art MRI for the longitudinal assessment of cystic fibrosis

JC Woods, JM Wild, MO Wielpütz… - Journal of Magnetic …, 2020‏ - Wiley Online Library
Pulmonary MRI can now provide high‐resolution images that are sensitive to early disease
and specific to inflammation in cystic fibrosis (CF) lung disease. With specificity and function …

PRAGMA-CF. A quantitative structural lung disease computed tomography outcome in young children with cystic fibrosis

T Rosenow, MCJ Oudraad, CP Murray… - American journal of …, 2015‏ - atsjournals.org
Rationale: Chest computed tomography (CT) is the gold standard for demonstrating cystic
fibrosis (CF) airway disease. However, there are no standardized outcome measures …

Lung clearance index and structural lung disease on computed tomography in early cystic fibrosis

KA Ramsey, T Rosenow, L Turkovic… - American journal of …, 2016‏ - atsjournals.org
Rationale: The lung clearance index is a measure of ventilation distribution derived from the
multiple-breath washout technique. It has been suggested as a surrogate for chest …

Early lung disease in infants and preschool children with cystic fibrosis. What have we learned and what should we do about it?

SC Ranganathan, GL Hall, PD Sly, SM Stick… - American journal of …, 2017‏ - atsjournals.org
The past decade has seen significant advances in understanding of the pathogenesis and
progression of lung disease in cystic fibrosis (CF). Pulmonary inflammation, infection, and …

The effect of inhaled hypertonic saline on lung structure in children aged 3–6 years with cystic fibrosis (SHIP-CT): a multicentre, randomised, double-blind, controlled …

HAWM Tiddens, Y Chen, ER Andrinopoulou… - The lancet Respiratory …, 2022‏ - thelancet.com
Summary Background In the Saline Hypertonic in Preschoolers (SHIP) study, inhaled 7%
hypertonic saline improved the lung clearance index in children aged 3–6 years with cystic …

Functional imaging of the lungs with gas agents

SJ Kruger, SK Nagle, MJ Couch, Y Ohno… - Journal of Magnetic …, 2016‏ - Wiley Online Library
This review focuses on the state‐of‐the‐art of the three major classes of gas contrast agents
used in magnetic resonance imaging (MRI)—hyperpolarized (HP) gas, molecular oxygen …

Imaging of cystic fibrosis lung disease and clinical interpretation

MO Wielpütz, M Eichinger, J Biederer… - RöFo-Fortschritte auf …, 2016‏ - thieme-connect.com
Progressive lung disease in cystic fibrosis (CF) is the life-limiting factor of this autosomal
recessive genetic disorder. Increasing implementation of CF newborn screening allows for a …

Update on the role of chest imaging in cystic fibrosis

SM Bugenhagen, JCE Grant, DB Rosenbluth… - Radiographics, 2024‏ - pubs.rsna.org
Cystic fibrosis is a genetic disease with multisystem involvement and associated morbidity
and mortality that are most directly related to progressive lung disease. The hallmark …

State-of-the-art review of lung imaging in cystic fibrosis with recommendations for pulmonologists and radiologists from the “iMAging managEment of cySTic fibROsis” …

P Ciet, S Bertolo, M Ros, R Casciaro… - European …, 2022‏ - publications.ersnet.org
Objective Imaging represents an important noninvasive means to assess cystic fibrosis (CF)
lung disease, which remains the main cause of morbidity and mortality in CF patients. While …