Synovial sarcoma: a clinical review

AM Gazendam, S Popovic, S Munir, N Parasu… - Current …, 2021 - mdpi.com
Synovial sarcomas (SS) represent a unique subset of soft tissue sarcomas (STS) and
account for 5–10% of all STS. Synovial sarcoma differs from other STS by the relatively …

Synovial sarcoma: current concepts and future perspectives

S Stacchiotti, BA Van Tine - Journal of clinical oncology, 2018 - ascopubs.org
Synovial sarcoma (SS) is a rare sarcoma driven by a translocation between SS18 and SSX
1, 2, or 4. With approximately 800 to 1,000 cases a year in the United States, it most …

Local therapy in localized Ewing tumors: results of 1058 patients treated in the CESS 81, CESS 86, and EICESS 92 trials

A Schuck, S Ahrens, M Paulussen, M Kuhlen… - International Journal of …, 2003 - Elsevier
Purpose: The impact of different local therapy approaches on local control, event-free
survival, and secondary malignancies in the CESS 81, CESS 86, and EICESS 92 trials was …

[PDF][PDF] Pediatric non-rhabdomyosarcoma soft tissue sarcomas: standard of care and treatment recommendations from the European Paediatric Soft Tissue Sarcoma …

A Ferrari, B Brennan, M Casanova… - Cancer Management …, 2022 - Taylor & Francis
This paper describes the standard of care for patients with non-rhabdomyosarcoma soft
tissue sarcomas (NRSTS) and the therapeutic recommendations developed by the …

Soft tissue sarcomas in adolescents and young adults: a comparison with their paediatric and adult counterparts

WTA van der Graaf, D Orbach, IR Judson… - The Lancet …, 2017 - thelancet.com
Survival outcomes for adolescent and young adult patients with soft tissue sarcomas lag
behind those of children diagnosed with histologically similar tumours. To help understand …

MRI of rhabdomyosarcoma and other soft-tissue sarcomas in children

EJ Inarejos Clemente, M Navallas… - Radiographics, 2020 - pubs.rsna.org
Soft-tissue sarcomas in children comprise a heterogeneous group of entities with variable
manifestation depending on the age of the patient and the location of the tumor. MRI is the …

SMARCB1-deficient Tumors of Childhood: A Practical Guide

BR Pawel - Pediatric and Developmental Pathology, 2018 - journals.sagepub.com
The SMARCB1 gene (INI1, BAF47) is a member of the SWItch/Sucrose Non-Fermentable
(SWI/SNF) chromatin remodeling complex, involved in the epigenetic regulation of gene …

Systemic treatment for adults with synovial sarcoma

IME Desar, EDG Fleuren… - Current treatment options …, 2018 - Springer
Opinion Statement Synovial sarcoma (SS) is a rare, yet highly malignant, type of soft tissue
sarcoma (STS), for which survival has not improved significantly during the past years. In this …

Paediatric non-rhabdomyosarcoma soft tissue sarcomas: the prospective NRSTS 2005 study by the European Pediatric Soft Tissue Sarcoma Study Group (EpSSG)

A Ferrari, MM van Noesel, B Brennan… - The Lancet Child & …, 2021 - thelancet.com
Background A standardised approach to treatment of paediatric non-rhabdomyosarcoma
soft tissue sarcomas (NRSTS), which account for about 4% of childhood cancers, is still …

[HTML][HTML] Synovial sarcoma: characteristics, challenges, and evolving therapeutic strategies

JY Blay, M von Mehren, RL Jones, J Martin-Broto… - ESMO open, 2023 - Elsevier
Synovial sarcoma (SS) is a rare and aggressive disease that accounts for 5%-10% of all soft
tissue sarcomas. Although it can occur at any age, it typically affects younger adults and …