Brain energy and oxygen metabolism: emerging role in normal function and disease

ME Watts, R Pocock, C Claudianos - Frontiers in molecular …, 2018‏ - frontiersin.org
Dynamic metabolic changes occurring in neurons are critically important in directing brain
plasticity and cognitive function. In other tissue types, disruptions to metabolism and the …

[HTML][HTML] α-Synuclein misfolding and Parkinson's disease

L Breydo, JW Wu, VN Uversky - … et Biophysica Acta (BBA)-Molecular Basis …, 2012‏ - Elsevier
Substantial evidence links α-synuclein, a small highly conserved presynaptic protein with
unknown function, to both familial and sporadic Parkinson's disease (PD). α-Synuclein has …

The Lewy body in Parkinson's disease and related neurodegenerative disorders

K Wakabayashi, K Tanji, S Odagiri, Y Miki, F Mori… - Molecular …, 2013‏ - Springer
The histopathological hallmark of Parkinson's disease (PD) is the presence of fibrillar
aggregates referred to as Lewy bodies (LBs), in which α-synuclein is a major constituent …

Therapeutics in the pipeline targeting α-synuclein for Parkinson's disease

HG Jasutkar, SE Oh, MM Mouradian, E Barker - Pharmacological reviews, 2022‏ - Elsevier
Parkinson's disease (PD) is the second most common neurodegenerative disorder and the
fastest growing neurologic disease in the world, yet no disease-modifying therapy is …

Repression of α-synuclein expression and toxicity by microRNA-7

E Junn, KW Lee, BS Jeong, TW Chan, JY Im… - Proceedings of the …, 2009‏ - pnas.org
α-Synuclein is a key protein in Parkinson's disease (PD) because it accumulates as fibrillar
aggregates in pathologic hallmark features in affected brain regions, most notably in nigral …

Human physiomimetic model integrating microphysiological systems of the gut, liver, and brain for studies of neurodegenerative diseases

M Trapecar, E Wogram, D Svoboda, C Communal… - Science …, 2021‏ - science.org
Slow progress in the fight against neurodegenerative diseases (NDs) motivates an urgent
need for highly controlled in vitro systems to investigate organ-organ–and organ-immune …

The Lewy body in Parkinson's disease: molecules implicated in the formation and degradation of α‐synuclein aggregates

K Wakabayashi, K Tanji, F Mori, H Takahashi - Neuropathology, 2007‏ - Wiley Online Library
The histological hallmark of Parkinson's disease (PD) is the presence of fibrillar aggregates
called Lewy bodies (LBs). LB formation has been considered to be a marker for neuronal …

Neuropathology, biochemistry, and biophysics of α‐synuclein aggregation

VN Uversky - Journal of neurochemistry, 2007‏ - Wiley Online Library
Aggregation of α‐synuclein, an abundant and conserved pre‐synaptic brain protein, is
implicated as a critical factor in several neurodegenerative diseases. These diseases …

[HTML][HTML] Role of transglutaminase 2 in cell death, survival, and fibrosis

H Tatsukawa, K Hitomi - Cells, 2021‏ - mdpi.com
Transglutaminase 2 (TG2) is a ubiquitously expressed enzyme catalyzing the crosslinking
between Gln and Lys residues and involved in various pathophysiological events. Besides …

Hsp70 reduces α-synuclein aggregation and toxicity

J Klucken, Y Shin, E Masliah, BT Hyman… - Journal of Biological …, 2004‏ - jbc.org
Aggregation and cytotoxicity of misfolded α-synuclein is postulated to be crucial in the
disease process of neurodegenerative disorders such as Parkinson's disease and DLB …