[HTML][HTML] Mitochondrial pharmacology

RAJ Smith, RC Hartley, HM Cocheme… - Trends in pharmacological …, 2012‏ - cell.com
Mitochondria are being recognized as key factors in many unexpected areas of biomedical
science. In addition to their well-known roles in oxidative phosphorylation and metabolism, it …

Emerging therapies for mitochondrial diseases

M Hirano, V Emmanuele, CM Quinzii - Essays in biochemistry, 2018‏ - portlandpress.com
For the vast majority of patients with mitochondrial diseases, only supportive and
symptomatic therapies are available. However, in the last decade, due to extraordinary …

Mitochondrial ROS produced via reverse electron transport extend animal lifespan

F Scialo, A Sriram, D Fernandez-Ayala, N Gubina… - Cell metabolism, 2016‏ - cell.com
Increased production of reactive oxygen species (ROS) has long been considered a cause
of aging. However, recent studies have implicated ROS as essential secondary messengers …

[HTML][HTML] Oxidative metabolism drives immortalization of neural stem cells during tumorigenesis

F Bonnay, A Veloso, V Steinmann, T Köcher… - Cell, 2020‏ - cell.com
Metabolic reprogramming is a key feature of many cancers, but how and when it contributes
to tumorigenesis remains unclear. Here we demonstrate that metabolic reprogramming …

Mitochondrial complex I activity and NAD+/NADH balance regulate breast cancer progression

AF Santidrian, A Matsuno-Yagi, M Ritland… - The Journal of clinical …, 2013‏ - jci.org
Despite advances in clinical therapy, metastasis remains the leading cause of death in
breast cancer patients. Mutations in mitochondrial DNA, including those affecting complex I …

Superoxide is produced by the reduced flavin in mitochondrial complex I: a single, unified mechanism that applies during both forward and reverse electron transfer

KR Pryde, J Hirst - Journal of Biological Chemistry, 2011‏ - jbc.org
NADH ubiquinone oxidoreductase (complex I) is a major source of reactive oxygen species
in mitochondria and a contributor to cellular oxidative stress. In isolated complex I the …

Ndufs4 knockout mouse models of Leigh syndrome: pathophysiology and intervention

MAE Van De Wal, MJW Adjobo-Hermans, J Keijer… - Brain, 2022‏ - academic.oup.com
Mitochondria are small cellular constituents that generate cellular energy (ATP) by oxidative
phosphorylation (OXPHOS). Dysfunction of these organelles is linked to a heterogeneous …

Branched-chain amino acids, mitochondrial biogenesis, and healthspan: an evolutionary perspective

A Valerio, G D'Antona, E Nisoli - Aging (albany NY), 2011‏ - pmc.ncbi.nlm.nih.gov
Malnutrition is common among older persons, with important consequences increasing
frailty and morbidity and reducing health expectancy. On the contrary, calorie restriction (CR …

The advanced lipoxidation end-product malondialdehyde-lysine in aging and longevity

M Jové, N Mota-Martorell, I Pradas, M Martín-Gari… - Antioxidants, 2020‏ - mdpi.com
The nonenzymatic adduction of malondialdehyde (MDA) to the protein amino groups leads
to the formation of malondialdehyde-lysine (MDALys). The degree of unsaturation of …

[HTML][HTML] Physiologic implications of reactive oxygen species production by mitochondrial complex I reverse electron transport

JO Onukwufor, BJ Berry, AP Wojtovich - Antioxidants, 2019‏ - mdpi.com
Mitochondrial reactive oxygen species (ROS) can be either detrimental or beneficial
depending on the amount, duration, and location of their production. Mitochondrial complex I …