Inflammation and immunity in the pathogenesis of pulmonary arterial hypertension

M Rabinovitch, C Guignabert, M Humbert… - Circulation …, 2014‏ - ahajournals.org
This review summarizes an expanding body of knowledge indicating that failure to resolve
inflammation and altered immune processes underlie the development of pulmonary arterial …

Genetics and genomics of pulmonary arterial hypertension

F Soubrier, WK Chung, R Machado, E Grünig… - Journal of the American …, 2013‏ - jacc.org
Major discoveries have been obtained within the last decade in the field of hereditary
predisposition to pulmonary arterial hypertension (PAH). Among them, the identification of …

Immune and inflammatory cell involvement in the pathology of idiopathic pulmonary arterial hypertension

R Savai, SS Pullamsetti, J Kolbe, E Bieniek… - American journal of …, 2012‏ - atsjournals.org
Rationale: Pulmonary arterial hypertension (PAH) is characterized by vasoconstriction and
vascular remodeling. Recent studies have revealed that immune and inflammatory …

Inflammation in pulmonary arterial hypertension

LC Price, SJ Wort, F Perros, P Dorfmüller, A Huertas… - Chest, 2012‏ - Elsevier
Pulmonary arterial hypertension (PAH) is characterized by pulmonary vascular remodeling
of the precapillary pulmonary arteries, with excessive proliferation of vascular cells. Although …

Interleukin-6 overexpression induces pulmonary hypertension

MK Steiner, OL Syrkina, N Kolliputi, EJ Mark… - Circulation …, 2009‏ - ahajournals.org
Inflammatory cytokine interleukin (IL)-6 is elevated in the serum and lungs of patients with
pulmonary artery hypertension (PAH). Several animal models of PAH cite the potential role …

Inflammation, growth factors, and pulmonary vascular remodeling

PM Hassoun, L Mouthon, JA Barberà… - Journal of the american …, 2009‏ - jacc.org
Inflammatory processes are prominent in various types of human and experimental
pulmonary hypertension (PH) and are increasingly recognized as major pathogenic …

Molecular pathogenesis of pulmonary arterial hypertension

M Rabinovitch - The Journal of clinical investigation, 2012‏ - jci.org
Recent clinical and experimental studies are redefining the cellular and molecular bases of
pulmonary arterial hypertension (PAH). The genetic abnormalities first identified in …

Interleukin-6/interleukin-21 signaling axis is critical in the pathogenesis of pulmonary arterial hypertension

T Hashimoto-Kataoka, N Hosen, T Sonobe… - Proceedings of the …, 2015‏ - pnas.org
IL-6 is a multifunctional proinflammatory cytokine that is elevated in the serum of patients
with pulmonary arterial hypertension (PAH) and can predict the survival of patients with …

The role of vasculature and angiogenesis in respiratory diseases

M Ackermann, C Werlein, E Plucinski, S Leypold… - Angiogenesis, 2024‏ - Springer
In European countries, nearly 10% of all hospital admissions are related to respiratory
diseases, mainly chronic life-threatening diseases such as COPD, pulmonary hypertension …

Mechanisms of pulmonary vascular dysfunction in pulmonary hypertension and implications for novel therapies

H Christou, RA Khalil - American Journal of Physiology …, 2022‏ - journals.physiology.org
Pulmonary hypertension (PH) is a serious disease characterized by various degrees of
pulmonary vasoconstriction and progressive fibroproliferative remodeling and inflammation …