Importance Interstitial lung disease (ILD) consists of a group of pulmonary disorders
characterized by inflammation and/or fibrosis of the lung parenchyma associated with …

Pirfenidone and Nintedanib are specific drugs used against idiopathic pulmonary fibrosis
(IPF) that showed efficacy in non-IPF fibrosing interstitial lung diseases (ILD). Both drugs …

Systemic sclerosis (SSc) is a complex autoimmune disease characterized by vascular
damage, vasoinstability, and decreased perfusion with ischemia, inflammation, and …

This guideline was developed according to the British Society for Rheumatology Guidelines
Protocol by a Guideline Development Group comprising healthcare professionals with …

Background: The American Thoracic Society (ATS) convened an international,
multidisciplinary panel to develop clinical practice guidelines for the treatment of systemic …

Lysophosphatidic acid (LPA)-mediated activation of LPA receptor 1 (LPAR1) contributes to
the pathophysiology of fibrotic diseases such as idiopathic pulmonary fibrosis (IPF) and …

Background Clinical guidance on the identification and management of connective tissue
disease-associated interstitial lung disease (CTD-ILD) is needed for optimal clinical practice …

Systemic sclerosis (SSc) is a rare autoimmune disease characterized by a tripod combining
vasculopathy, fibrosis, and immune-mediated inflammatory processes. The prevalence of …

Background: The American Thoracic Society convened an international, multidisciplinary
panel to develop clinical practice guidelines for the treatment of systemic sclerosis …

Updates on interstitial lung disease and other selected extr... : Current Opinion in Rheumatology
Updates on interstitial lung disease and other selected extra-articular manifestations of …