Idiopathic pulmonary fibrosis

TE King, A Pardo, M Selman - The Lancet, 2011 - thelancet.com
Idiopathic pulmonary fibrosis is a devastating, age-related lung disease of unknown cause
that has few treatment options. This disease was once thought to be a chronic inflammatory …

Targeting extracellular matrix stiffness to attenuate disease: From molecular mechanisms to clinical trials

MC Lampi, CA Reinhart-King - Science translational medicine, 2018 - science.org
Tissues stiffen during aging and during the pathological progression of cancer, fibrosis, and
cardiovascular disease. Extracellular matrix stiffness is emerging as a prominent mechanical …

Single-cell transcriptomic analysis of human lung provides insights into the pathobiology of pulmonary fibrosis

PA Reyfman, JM Walter, N Joshi… - American journal of …, 2019 - atsjournals.org
Rationale: The contributions of diverse cell populations in the human lung to pulmonary
fibrosis pathogenesis are poorly understood. Single-cell RNA sequencing can reveal …

Single-cell RNA sequencing reveals profibrotic roles of distinct epithelial and mesenchymal lineages in pulmonary fibrosis

AC Habermann, AJ Gutierrez, LT Bui, SL Yahn… - Science …, 2020 - science.org
Pulmonary fibrosis (PF) is a form of chronic lung disease characterized by pathologic
epithelial remodeling and accumulation of extracellular matrix (ECM). To comprehensively …

Diagnosis and evaluation of hypersensitivity pneumonitis: CHEST guideline and expert panel report

ERF Pérez, WD Travis, DA Lynch, KK Brown… - Chest, 2021 - Elsevier
Background The purpose of this analysis is to provide evidence-based and consensus-
derived guidance for clinicians to improve individual diagnostic decision-making for …

Hypersensitivity pneumonitis: perspectives in diagnosis and management

M Vasakova, F Morell, S Walsh, K Leslie… - American journal of …, 2017 - atsjournals.org
Awareness of hypersensitivity pneumonitis (HP) as a unique disease entity dates back to the
18th century (1). Since then, numerous inciting agents have been attributed to inducing HP …

Hypersensitivity pneumonitis: insights in diagnosis and pathobiology

M Selman, A Pardo, TE King Jr - American journal of respiratory …, 2012 - atsjournals.org
Hypersensitivity pneumonitis (HP) is a complex syndrome resulting from repeated exposure
to a variety of organic particles. HP may present as acute, subacute, or chronic clinical forms …

Hypersensitivity pneumonitis

U Costabel, Y Miyazaki, A Pardo, D Koschel… - Nature Reviews …, 2020 - nature.com
Hypersensitivity pneumonitis (HP) is a complex syndrome caused by the inhalation of a
variety of antigens in susceptible and sensitized individuals. These antigens are found in the …

Immune mechanisms in pulmonary fibrosis

S Kolahian, IE Fernandez, O Eickelberg… - American journal of …, 2016 - atsjournals.org
Pulmonary fibrosis, particularly idiopathic pulmonary fibrosis, represents a chronic and
progressive disease with high mortality and limited therapeutic options. Excessive …

Antifibrotic activities of pirfenidone in animal models

CJ Schaefer, DW Ruhrmund, L Pan… - European …, 2011 - Eur Respiratory Soc
Pirfenidone is an orally active small molecule that has recently been evaluated in large
clinical trials for the treatment of idiopathic pulmonary fibrosis, a fatal disease in which the …