Adrenocortical carcinoma: current state of the art, ongoing controversies, and future directions in diagnosis and treatment

OA Shariq, TJ McKenzie - Therapeutic Advances in Chronic …, 2021 - journals.sagepub.com
Adrenocortical carcinoma (ACC) is a rare, aggressive malignancy with an annual incidence
of~ 1 case per million population. Differentiating between ACC and benign adrenocortical …

European Society of Endocrinology Clinical Practice Guidelines on the management of adrenocortical carcinoma in adults, in collaboration with the European Network …

M Fassnacht, OM Dekkers, T Else… - European journal of …, 2018 - academic.oup.com
Adrenocortical carcinoma (ACC) is a rare and in most cases steroid hormone-producing
tumor with variable prognosis. The purpose of these guidelines is to provide clinicians with …

Management of endocrine disease: adrenocortical carcinoma: differentiating the good from the poor prognosis tumors

A Jouinot, J Bertherat - European Journal of Endocrinology, 2018 - academic.oup.com
Adrenocortical carcinoma (ACC) is a rare malignancy with a poor prognosis, the five-years
overall survival being below 40%. However, there is great variability of outcomes and we …

Targeted molecular analysis in adrenocortical carcinomas: a strategy toward improved personalized prognostication

J Lippert, S Appenzeller, R Liang… - The Journal of …, 2018 - academic.oup.com
Context Adrenocortical carcinoma (ACC) has a heterogeneous prognosis, and current
medical therapies have limited efficacy in its advanced stages. Genome-wide multiomics …

Adjuvant therapy in adrenocortical carcinoma: reflections and future directions

S Bedrose, M Daher, L Altameemi, MA Habra - Cancers, 2020 - mdpi.com
Adrenocortical carcinoma (ACC) is a rare and aggressive malignancy with high risk of
recurrence despite macroscopically complete surgical resection. The main predictors of …

Laparoscopic versus open adrenalectomy for localized (stage 1/2) adrenocortical carcinoma: experience at a single, high-volumecenter

K Wu, Z Liu, J Liang, Y Tang, Z Zou, C Zhou, F Zhang… - Surgery, 2018 - Elsevier
Background Open adrenalectomy is considered a standard operative approach for
adrenocortical carcinoma, and laparoscopic adrenalectomy remains controversial. We …

[HTML][HTML] A Review on Mitotane: A Target Therapy in Adrenocortical Carcinoma

F Flauto, MC De Martino, C Vitiello, R Pivonello… - Cancers, 2024 - mdpi.com
Adrenocortical carcinomas (ACCs) are rare and aggressive malignancies of adrenal cortex,
associated with largely unknown mechanisms of biological development and poor …

Open versus laparoscopic surgery in the management of adrenocortical carcinoma: a systematic review and meta-analysis

H Nakanishi, S Miangul, R Wang, J El Haddad… - Annals of Surgical …, 2023 - Springer
Background Laparoscopic surgery is considered a standard treatment for benign adrenal
tumors; however, no consensus has been reached on the optimal resection technique for …

Surgery for adrenocortical carcinoma: When and how?

TJ Sinclair, A Gillis, WM Alobuia, H Wild… - Best Practice & Research …, 2020 - Elsevier
Adrenocortical carcinoma (ACC) is a rare malignancy that is frequently asymptomatic at
presentation, yet has a high rate of metastatic disease at the time of diagnosis. Prognosis is …

Prognostic factors for adrenocortical carcinoma outcomes

C Scollo, M Russo, MA Trovato, D Sambataro… - Frontiers in …, 2016 - frontiersin.org
Purpose Adrenocortical carcinoma (ACC) is an aggressive tumor characterized by a high
recurrence rate and poor response to treatment. This study analyzes a consecutive series of …