Dilated cardiomyopathy: causes, mechanisms, and current and future treatment approaches

S Heymans, NK Lakdawala, C Tschöpe, K Klingel - The Lancet, 2023 - thelancet.com
Dilated cardiomyopathy is conventionally defined as the presence of left ventricular or
biventricular dilatation or systolic dysfunction in the absence of abnormal loading conditions …

Phospholamban R14del disease: The past, the present and the future

E Vafiadaki, PC Glijnis, PA Doevendans… - Frontiers in …, 2023 - frontiersin.org
Arrhythmogenic cardiomyopathy affects significant number of patients worldwide and is
characterized by life-threatening ventricular arrhythmias and sudden cardiac death …

Aberrant PLN-R14del Protein Interactions Intensify SERCA2a Inhibition, Driving Impaired Ca2+ Handling and Arrhythmogenesis

E Vafiadaki, K Haghighi, DA Arvanitis… - International Journal of …, 2022 - mdpi.com
Phospholamban (PLN), a key modulator of Ca2+-homeostasis, inhibits sarcoplasmic
reticulum (SR) calcium-ATPase (SERCA2a) and regulates cardiac contractility. The human …

Bromuconazole exposure induces cardiotoxicity and lipid transport disorder in larval zebrafish

Z Qin, W Wang, Y Weng, Z Bao, G Yang… - … and Physiology Part C …, 2022 - Elsevier
Bromuconazole (BRO), as one of the typical triazole fungicides, has not been reported on its
effects on aquatic organisms. In this study, zebrafish embryos were used as experimental …

RBPMS2 is a myocardial-enriched splicing regulator required for cardiac function

AA Akerberg, M Trembley, V Butty… - Circulation …, 2022 - Am Heart Assoc
Background: RBPs (RNA-binding proteins) perform indispensable functions in the post-
transcriptional regulation of gene expression. Numerous RBPs have been implicated in …

Modeling human cardiac arrhythmias: insights from zebrafish

S Gauvrit, J Bossaer, J Lee, MM Collins - Journal of Cardiovascular …, 2022 - mdpi.com
Cardiac arrhythmia, or irregular heart rhythm, is associated with morbidity and mortality and
is described as one of the most important future public health challenges. Therefore …

[HTML][HTML] Early calcium and cardiac contraction defects in a model of phospholamban R9C mutation in zebrafish

M Vicente, J Salgado-Almario… - Journal of Molecular and …, 2022 - Elsevier
The phospholamban mutation Arg 9 to Cys (R9C) has been found to cause a dilated
cardiomyopathy in humans and in transgenic mice, with ventricular dilation and premature …

Early consequences of the phospholamban mutation PLN‐R14del+/− in a transgenic mouse model

C Maniezzi, M Eskandr, C Florindi, M Ferrandi… - Acta …, 2024 - Wiley Online Library
Aims The heterozygous phospholamban (PLN) mutation R14del (PLN R14del+/−) is
associated with a severe arrhythmogenic cardiomyopathy (ACM) develo** in the …

[HTML][HTML] Transient titin-dependent ventricular defects during development lead to adult atrial arrhythmia and impaired contractility

X Jiang, OT Ly, H Chen, Z Zhang, BA Ibarra, MA Pavel… - Iscience, 2024 - cell.com
Developmental causes of the most common arrhythmia, atrial fibrillation (AF), are poorly
defined, with compensation potentially masking arrhythmic risk. Here, we delete 9 amino …

An atrial fibrillation-associated regulatory region modulates cardiac Tbx5 levels and arrhythmia susceptibility

FM Bosada, K van Duijvenboden, AE Giovou… - Elife, 2023 - elifesciences.org
Heart development and rhythm control are highly Tbx5 dosage-sensitive. TBX5
haploinsufficiency causes congenital conduction disorders, whereas increased expression …