The variable in common variable immunodeficiency: a disease of complex phenotypes

S Jolles - The Journal of Allergy and Clinical Immunology: In …, 2013‏ - Elsevier
Common variable immunodeficiency (CVID) is the most common and clinically most
important severe primary antibody deficiency and is characterized by low levels of IgG, IgA …

Beyond the extra respiration of phagocytosis: NADPH oxidase 2 in adaptive immunity and inflammation

PM Mortimer, SA Mc Intyre, DC Thomas - Frontiers in Immunology, 2021‏ - frontiersin.org
Reactive oxygen species (ROS) derived from the phagocyte NADPH oxidase (NOX2) are
essential for host defence and immunoregulation. Their levels must be tightly controlled …

The EUROclass trial: defining subgroups in common variable immunodeficiency

C Wehr, T Kivioja, C Schmitt, B Ferry… - Blood, The Journal …, 2008‏ - ashpublications.org
The heterogeneity of common variable immunodeficiency (CVID) calls for a classification
addressing pathogenic mechanisms as well as clinical relevance. This European …

Reactive oxygen species deficiency induces autoimmunity with type 1 interferon signature

T Kelkka, D Kienhöfer, M Hoffmann, M Linja… - Antioxidants & redox …, 2014‏ - liebertpub.com
Aims: Chronic granulomatous disease (CGD) is a primary immunodeficiency caused by
mutations in the phagocyte reactive oxygen species (ROS)–producing NOX2 enzyme …

The plasma membrane: a platform for intra-and intercellular redox signaling

DE Nordzieke, I Medraño-Fernandez - Antioxidants, 2018‏ - mdpi.com
Membranes are of outmost importance to allow for specific signal transduction due to their
ability to localize, amplify, and direct signals. However, due to the double-edged nature of …

[HTML][HTML] Recent advances in chronic granulomatous disease

G Anjani, P Vignesh, V Joshi, JK Shandilya… - Genes & diseases, 2020‏ - Elsevier
Chronic granulomatous disease (CGD) is an inherited defect of phagocyte function due to
defective NADPH oxidase. Patients with CGD are not able to effectively clear the infections …

Inflammatory manifestations in chronic granulomatous disease (CGD)

SD Rosenzweig - Journal of Clinical Immunology, 2008‏ - Springer
Chronic granulomatous disease (CGD) is a genetically heterogeneous disease
characterized by recurrent life-threatening infections with bacteria and fungi as well as …

Differentiation of common variable immunodeficiency from IgG deficiency

CA Filion, S Taylor-Black, PJ Maglione… - The Journal of Allergy …, 2019‏ - Elsevier
Background Common variable immunodeficiency (CVID) and IgG deficiency are 2 of the
more prevalent primary humoral immune defects. The former is defined by consensus with …

T and B lymphocyte abnormalities in bone marrow biopsies of common variable immunodeficiency

MLG Ochtrop, S Goldacker, AM May… - Blood, The Journal …, 2011‏ - ashpublications.org
In common variable immunodeficiency (CVID) defects in early stages of B-cell development,
bone marrow (BM) plasma cells and T lymphocytes have not been studied systematically …

Reactive oxygen species: the signal regulator of B cell

H Zhang, L Wang, Y Chu - Free Radical Biology and Medicine, 2019‏ - Elsevier
Reactive oxygen species (ROS) are indispensable for determining the fate of immune cells
in both physiological and pathogenic environments, thus stimulating the interest of …