Factor XIII deficiency in Iran: a comprehensive review of the literature
Factor XIII deficiency (FXIIID) is a rare bleeding disorder with an estimated prevalence of 1 in
2-million population worldwide. In Iran, a Middle Eastern country with a high rate of …
2-million population worldwide. In Iran, a Middle Eastern country with a high rate of …
[HTML][HTML] Current understanding in diagnosis and management of factor XIII deficiency
Factor XIII or" fibrin-stabilizing factor," is a transglutaminase circulates in the blood
circulation as a hetero tetramer with two catalytic A subunits and two carrier B subunits. This …
circulation as a hetero tetramer with two catalytic A subunits and two carrier B subunits. This …
Clinical manifestations and management of life-threatening bleeding in the largest group of patients with severe factor XIII deficiency
Factor XIII (FXIII) deficiency is a rare hemorrhagic disorder for which the highest incidence
occurs in southeast Iran. The aim of this study was to assess molecular characteristics …
occurs in southeast Iran. The aim of this study was to assess molecular characteristics …
Congenital factor V deficiency: comparison of the severity of clinical presentations among patients with rare bleeding disorders
Abstract Background: Factor V deficiency (FVD) is a rare bleeding disorder (RBD) mostly
present in regions with a high rate of consanguinity. FVD after FXIII deficiency is the next …
present in regions with a high rate of consanguinity. FVD after FXIII deficiency is the next …
Central nervous system bleeding in pediatric patients with factor XIII deficiency: A study on 23 new cases
Abstract Background Factor XIII (FXIII) deficiency is an extremely rare bleeding disorder,
which has the highest incidence in Sistan and Baluchistan Province in Iran, compared to its …
which has the highest incidence in Sistan and Baluchistan Province in Iran, compared to its …
Challenges in implementation of ISTH diagnostic algorithm for diagnosis and classification of factor XIII deficiency in Iran
Factor XIII (FXIII) deficiency is an extremely rare hemorrhagic disorder with an~ 12-fold
higher incidence in Iran compared with the overall prevalence of the disorder [1] …
higher incidence in Iran compared with the overall prevalence of the disorder [1] …
Rare bleeding disorders: a narrative review of epidemiology, molecular and clinical presentations, diagnosis and treatment
Rare bleeding disorders (RBDs) are a heterogeneous group of disorders that account for 3-
5% of all inherited coagulation factor deficiencies. Most of these deficiencies were first …
5% of all inherited coagulation factor deficiencies. Most of these deficiencies were first …
Congenital combined bleeding disorders, a comprehensive study of a large number of Iranian patients
SE Ahmadi, M Jazebi, G Bahoush… - Clinical and Applied …, 2021 - journals.sagepub.com
Congenital combined bleeding disorders (CBDs) are extremely rare disorders which mainly
occur in regions with a high rate of consanguineous marriage. These disorders can present …
occur in regions with a high rate of consanguineous marriage. These disorders can present …
Establishment of a prenatal diagnosis schedule as part of a prophylaxis program of factor XIII deficiency in the southeast of Iran
M Naderi, SE Reykande, A Dorgalaleh… - Blood Coagulation & …, 2016 - journals.lww.com
Factor XIII deficiency (FXIIID) is an extremely rare bleeding disorder with a prevalence of 1 in
3 million in the general population. Compared to its global incidence, it has the greatest …
3 million in the general population. Compared to its global incidence, it has the greatest …
Congenital combined deficiency of coagulation factors: a study of seven patients
Combined deficiency of coagulation factors is considered as an extremely rare bleeding
disorder (RBD) inherited in an autosomal recessive pattern. This disorder is more likely to …
disorder (RBD) inherited in an autosomal recessive pattern. This disorder is more likely to …