Immunoglobulin light chain amyloidosis: 2020 update on diagnosis, prognosis, and treatment

MA Gertz - American journal of hematology, 2020 - Wiley Online Library
Abstract Disease Overview Immunoglobulin light chain amyloidosis is a clonal,
nonproliferative plasma cell disorder in which fragments of immunoglobulin light or heavy …

Recent advances in the diagnosis, risk stratification, and management of systemic light-chain amyloidosis

I Vaxman, M Gertz - Acta Haematologica, 2019 - karger.com
The term amyloidosis refers to a group of disorders in which protein fibrils accumulate in
certain organs, disrupt their tissue architecture, and impair the function of the effected organ …

Prognosis and staging of AL amyloidosis

T Dittrich, C Kimmich, U Hegenbart… - Acta haematologica, 2020 - karger.com
The treatment options for systemic light chain amyloidosis (AL) are currently widening in an
unprecedented way, brought about by an expanding arsenal of anti-myeloma therapy as …

Immunoglobulin light chain amyloidosis: 2018 Update on diagnosis, prognosis, and treatment

MA Gertz - American journal of hematology, 2018 - Wiley Online Library
Abstract Disease Overview Immunoglobulin light chain amyloidosis is a clonal,
nonproliferative plasma cell disorder in which fragments of immunoglobulin light or heavy …

Digoxin use in systemic light-chain (AL) amyloidosis: contra-indicated or cautious use?

E Muchtar, MA Gertz, SK Kumar, G Lin, B Boilson… - Amyloid, 2018 - Taylor & Francis
Aim: Digoxin is considered contraindicated in light-chain (AL) amyloidosis, given reports of
increased toxicity published 30–50 years ago. We sought to determine the frequency of …

New developments in diagnosis, risk assessment and management in systemic amyloidosis

I Vaxman, A Dispenzieri, E Muchtar, M Gertz - Blood reviews, 2020 - Elsevier
Amyloidosis is a group of disorders characterized by a misfolded protein that deposits in
organs and compromise their function. Clinician should have a high index of suspicion …

Ten‐year survivors in AL amyloidosis: characteristics and treatment pattern

E Muchtar, MA Gertz, MQ Lacy, RS Go… - British journal of …, 2019 - Wiley Online Library
Improvement in survival in Light chain (AL) amyloidosis has been seen over recent decades,
enabling more patients to achieve long‐term survival. Patients with AL amyloidosis who …

Bone marrow plasma cells 20% or greater discriminate presentation, response, and survival in AL amyloidosis

E Muchtar, MA Gertz, TV Kourelis, S Sidana, RS Go… - Leukemia, 2020 - nature.com
We explored the association between bone marrow plasma cells (BMPCs) and disease
presentation and outcome among 1574 AL patients. Three BMPC groups were formulated:< …

Biomarkers in AL amyloidosis

D Fotiou, F Theodorakakou, E Kastritis - International journal of molecular …, 2021 - mdpi.com
Systemic AL amyloidosis is a rare complex hematological disorder caused by clonal plasma
cells which produce amyloidogenic immunoglobulins. Outcome and prognosis is the …

Clinical considerations for immunoparesis in multiple myeloma

M Chahin, Z Branham, A Fox, C Leurinda… - Cancers, 2022 - mdpi.com
Simple Summary Immunoparesis in multiple myeloma is defined as the suppression of one
or more of the uninvolved immunoglobulins, AKA, polyclonal immunoglobulin. The extent of …