Molecular mechanisms of fragile X syndrome: a twenty-year perspective

MR Santoro, SM Bray, ST Warren - Annual Review of Pathology …, 2012 - annualreviews.org
Fragile X syndrome (FXS) is a common form of inherited intellectual disability and is one of
the leading known causes of autism. The mutation responsible for FXS is a large expansion …

Disruption of RNA metabolism in neurological diseases and emerging therapeutic interventions

JK Nussbacher, R Tabet, GW Yeo, C Lagier-Tourenne - Neuron, 2019 - cell.com
RNA binding proteins are critical to the maintenance of the transcriptome via controlled
regulation of RNA processing and transport. Alterations of these proteins impact multiple …

[HTML][HTML] A mammalian microRNA expression atlas based on small RNA library sequencing

P Landgraf, M Rusu, R Sheridan, A Sewer, N Iovino… - Cell, 2007 - cell.com
MicroRNAs (miRNAs) are small noncoding regulatory RNAs that reduce stability and/or
translation of fully or partially sequence-complementary target mRNAs. In order to identify …

[HTML][HTML] Regulation of synaptic structure and function by FMRP-associated microRNAs miR-125b and miR-132

D Edbauer, JR Neilson, KA Foster, CF Wang… - Neuron, 2010 - cell.com
MicroRNAs (miRNAs) are noncoding RNAs that suppress translation of specific mRNAs. The
miRNA machinery interacts with fragile X mental retardation protein (FMRP), which functions …

Psychosis and autism as diametrical disorders of the social brain

B Crespi, C Badcock - Behavioral and brain sciences, 2008 - cambridge.org
Autistic-spectrum conditions and psychotic-spectrum conditions (mainly schizophrenia,
bipolar disorder, and major depression) represent two major suites of disorders of human …

Existence of a microRNA pathway in anucleate platelets

P Landry, I Plante, DL Ouellet, MP Perron… - Nature structural & …, 2009 - nature.com
Platelets have a crucial role in the maintenance of hemostasis as well as in thrombosis and
vessel occlusion, which underlie stroke and acute coronary syndromes. Anucleate platelets …

MicroRNAs in disease and potential therapeutic applications

HS Soifer, JJ Rossi, P Sætrom - Molecular therapy, 2007 - cell.com
MicroRNAs (miRNAs) are 21–24 nucleotide (nt) duplex RNAs that are created from
precursor transcripts by subsequent processing steps mediated by members of the RNAseIII …

The pathophysiology of fragile X (and what it teaches us about synapses)

AL Bhakar, G Dölen, MF Bear - Annual review of neuroscience, 2012 - annualreviews.org
Fragile X is the most common known inherited cause of intellectual disability and autism,
and it typically results from transcriptional silencing of FMR1 and loss of the encoded …

Let me count the ways: mechanisms of gene regulation by miRNAs and siRNAs

L Wu, JG Belasco - Molecular cell, 2008 - cell.com
The downregulation of gene expression by miRNAs and siRNAs is a complex process
involving both translational repression and accelerated mRNA turnover, each of which …

[HTML][HTML] G-quadruplexes: Emerging roles in neurodegenerative diseases and the non-coding transcriptome

R Simone, P Fratta, S Neidle, GN Parkinson, AM Isaacs - FEBS letters, 2015 - Elsevier
G-rich sequences in DNA and RNA have a propensity to fold into stable secondary
structures termed G-quadruplexes. G-quadruplex forming sequences are widespread …