Eye movements in patients with neurodegenerative disorders

TJ Anderson, MR MacAskill - Nature Reviews Neurology, 2013 - nature.com
The neural pathways and brain regions involved in eye movements during ocular fixation
and gaze control include the cerebrum, brainstem and cerebellum, and abnormal eye …

Clinical features, neurogenetics and neuropathology of the polyglutamine spinocerebellar ataxias type 1, 2, 3, 6 and 7

U Rüb, L Schöls, H Paulson, G Auburger… - Progress in …, 2013 - Elsevier
The spinocerebellar ataxias type 1 (SCA1), 2 (SCA2), 3 (SCA3), 6 (SCA6) and 7 (SCA7) are
genetically defined autosomal dominantly inherited progressive cerebellar ataxias (ADCAs) …

Cerebellum and ocular motor control

A Kheradmand, DS Zee - Frontiers in neurology, 2011 - frontiersin.org
An intact cerebellum is a prerequisite for optimal ocular motor performance. The cerebellum
fine-tunes each of the subtypes of eye movements so they work together to bring and …

Biological and clinical characteristics of individuals at risk for spinocerebellar ataxia types 1, 2, 3, and 6 in the longitudinal RISCA study: analysis of baseline data

H Jacobi, K Reetz, ST du Montcel, P Bauer… - The Lancet …, 2013 - thelancet.com
Summary Background Spinocerebellar ataxias (SCAs) are autosomal, dominantly inherited,
fully penetrant neurodegenerative diseases. Our aim was to study the preclinical stage of the …

The preclinical stage of spinocerebellar ataxias

RP Maas, J van Gaalen, T Klockgether… - Neurology, 2015 - neurology.org
The autosomal dominant spinocerebellar ataxias (SCAs) are a heterogeneous group of
degenerative diseases of the cerebellum and connected regions. The discovery of various …

Alterations of eye movement control in neurodegenerative movement disorders

M Gorges, EH Pinkhardt… - Journal of ophthalmology, 2014 - Wiley Online Library
The evolution of the fovea centralis, the most central part of the retina and the area of the
highest visual accuracy, requires humans to shift their gaze rapidly (saccades) to bring some …

Spinocerebellar ataxia type 2: clinical presentation, molecular mechanisms, and therapeutic perspectives

JJ Magana, L Velázquez-Pérez, B Cisneros - Molecular neurobiology, 2013 - Springer
Abstract Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant genetic disease
characterized by cerebellar dysfunction associated with slow saccades, early hyporeflexia …

A comprehensive review of spinocerebellar ataxia type 2 in Cuba

L Velázquez-Pérez, R Rodríguez-Labrada… - The Cerebellum, 2011 - Springer
Abstract Spinocerebellar ataxia type 2 (SCA2) is an autosomal dominant cerebellar ataxia
characterized by a progressive cerebellar syndrome associated to saccadic slowing …

Progression of early features of spinocerebellar ataxia type 2 in individuals at risk: a longitudinal study

L Velázquez-Pérez, R Rodríguez-Labrada… - The Lancet …, 2014 - thelancet.com
Background The effects of ATXN2 expansion on the nervous system arise before the
cerebellar syndrome can be diagnosed; however, progression of the underlying early …