State-of-the-art strategies for targeting the DNA damage response in cancer

PG Pilié, C Tang, GB Mills, TA Yap - Nature reviews Clinical oncology, 2019‏ - nature.com
Genomic instability is a key hallmark of cancer that arises owing to defects in the DNA
damage response (DDR) and/or increased replication stress. These alterations promote the …

Genome-wide association studies of cancer: current insights and future perspectives

A Sud, B Kinnersley, RS Houlston - Nature Reviews Cancer, 2017‏ - nature.com
Genome-wide association studies (GWAS) provide an agnostic approach for investigating
the genetic basis of complex diseases. In oncology, GWAS of nearly all common …

[HTML][HTML] Pathogenic germline variants in 10,389 adult cancers

K Huang, RJ Mashl, Y Wu, DI Ritter, J Wang, C Oh… - Cell, 2018‏ - cell.com
We conducted the largest investigation of predisposition variants in cancer to date,
discovering 853 pathogenic or likely pathogenic variants in 8% of 10,389 cases from 33 …

Clinical sequencing of soft tissue and bone sarcomas delineates diverse genomic landscapes and potential therapeutic targets

BA Nacev, F Sanchez-Vega, SA Smith… - Nature …, 2022‏ - nature.com
The genetic, biologic, and clinical heterogeneity of sarcomas poses a challenge for the
identification of therapeutic targets, clinical research, and advancing patient care. Because …

Germline and somatic genetics of osteosarcoma—connecting aetiology, biology and therapy

DM Gianferante, L Mirabello, SA Savage - Nature Reviews …, 2017‏ - nature.com
Clinical outcomes and treatment modalities for osteosarcoma, the most common primary
cancer of bone, have changed very little over the past 30 years. The peak incidence of …

Therapy-related myeloid neoplasms: when genetics and environment collide

ME McNerney, LA Godley, MM Le Beau - Nature Reviews Cancer, 2017‏ - nature.com
Therapy-related myeloid neoplasms (t-MN) arise as a late effect of chemotherapy and/or
radiation administered for a primary condition, typically a malignant disease, solid organ …

Frequency of pathogenic germline variants in cancer-susceptibility genes in patients with osteosarcoma

L Mirabello, B Zhu, R Koster, E Karlins, M Dean… - JAMA …, 2020‏ - jamanetwork.com
Importance Osteosarcoma, the most common malignant bone tumor in children and
adolescents, occurs in a high number of cancer predisposition syndromes that are defined …

Childhood cancer predisposition syndromes—a concise review and recommendations by the Cancer Predisposition Working Group of the Society for Pediatric …

T Ripperger, SS Bielack, A Borkhardt… - American journal of …, 2017‏ - Wiley Online Library
Heritable predisposition is an important cause of cancer in children and adolescents.
Although a large number of cancer predisposition genes and their associated syndromes …

UK guidelines for the management of soft tissue sarcomas

AJ Hayes, IF Nixon, DC Strauss, BM Seddon… - British Journal of …, 2024‏ - nature.com
Soft tissue sarcomas (STS) are rare tumours arising in mesenchymal tissues and can occur
almost anywhere in the body. Their rarity, and the heterogeneity of subtype and location …

Adult-onset cancer predisposition syndromes in children and adolescents—to test or not to test?

CP Kratz, PJ Lupo, K Zelley, J Schienda… - Clinical Cancer …, 2024‏ - aacrjournals.org
With the increasing use of comprehensive germline genetic testing of children and
adolescents with cancer, it has become evident that pathogenic variants (PV) in adult-onset …