Meiotic recombination: the essence of heredity

N Hunter - Cold Spring Harbor perspectives in biology, 2015 - cshperspectives.cshlp.org
The study of homologous recombination has its historical roots in meiosis. In this context,
recombination occurs as a programmed event that culminates in the formation of crossovers …

Structural variation in the human genome and its role in disease

P Stankiewicz, JR Lupski - Annual review of medicine, 2010 - annualreviews.org
During the last quarter of the twentieth century, our knowledge about human genetic
variation was limited mainly to the heterochromatin polymorphisms, large enough to be …

Global variation in copy number in the human genome

R Redon, S Ishikawa, KR Fitch, L Feuk, GH Perry… - nature, 2006 - nature.com
Copy number variation (CNV) of DNA sequences is functionally significant but has yet to be
fully ascertained. We have constructed a first-generation CNV map of the human genome …

Genome architecture, rearrangements and genomic disorders

P Stankiewicz, JR Lupski - TRENDS in Genetics, 2002 - cell.com
An increasing number of human diseases are recognized to result from recurrent DNA
rearrangements involving unstable genomic regions. These are termed genomic disorders …

Segmental duplications and copy-number variation in the human genome

AJ Sharp, DP Locke, SD McGrath, Z Cheng… - The American Journal of …, 2005 - cell.com
The human genome contains numerous blocks of highly homologous duplicated sequence.
This higher-order architecture provides a substrate for recombination and recurrent …

Genomic disorders: structural features of the genome can lead to DNA rearrangements and human disease traits

JR Lupski - Trends in genetics, 1998 - cell.com
Molecular medicine began with Pauling's seminal work, which recognized sickle-cell
anemia as a molecular disease, and with Ingram's demonstration of a specific chemical …

Genomic disorders: molecular mechanisms for rearrangements and conveyed phenotypes

JR Lupski, P Stankiewicz - PLoS genetics, 2005 - journals.plos.org
Rearrangements of our genome can be responsible for inherited as well as sporadic traits.
The analyses of chromosome breakpoints in the proximal short arm of Chromosome 17 …

Chromosome 22-specific low copy repeats and the 22q11. 2 deletion syndrome: genomic organization and deletion endpoint analysis

TH Shaikh, H Kurahashi, SC Saitta… - Human molecular …, 2000 - academic.oup.com
The 22q11. 2 deletion syndrome, which includes DiGeorge and velocardiofacial syndromes
(DGS/VCFS), is the most common microdeletion syndrome. The majority of deleted patients …

[HTML][HTML] Exome sequence analysis suggests that genetic burden contributes to phenotypic variability and complex neuropathy

C Gonzaga-Jauregui, T Harel, T Gambin, M Kousi… - Cell reports, 2015 - cell.com
Summary Charcot-Marie-Tooth (CMT) disease is a clinically and genetically heterogeneous
distal symmetric polyneuropathy. Whole-exome sequencing (WES) of 40 individuals from 37 …

Cognitive performance among carriers of pathogenic copy number variants: analysis of 152,000 UK Biobank subjects

KM Kendall, E Rees, V Escott-Price, M Einon… - Biological …, 2017 - Elsevier
Abstract Background The UK Biobank is a unique resource for biomedical research, with
extensive phenotypic and genetic data on half a million adults from the general population …