Biliary atresia (BA) is a progressive, fibro‐obliterative disorder of the intrahepatic and
extrahepatic bile ducts in infancy. The majority of affected children will eventually develop …

Each Association appointed at least one author to serve on the writing group. The Chair of
the writing group was appointed by the AASLD. Members of the writing group were not …

MIM 263200) is a severe, typically early-onset form of cystic disease that primarily involves
the kidneys and biliary tract. Phenotypic expression and age at presentation can be quite …

Approaches to the management of portal hypertension and variceal hemorrhage in
pediatrics remain controversial, in large part because they are not well informed by rigorous …

The broad spectrum of hepatobiliary involvement in cystic fibrosis (CF) has been commonly
referred to as cystic fibrosis liver disease (CFLD). However, differences in the definitions of …

There are many causes of gastrointestinal bleeding (GIB) in children, and this condition is
not rare, having a reported incidence of 6.4%. Causes vary with age, but show considerable …

Several conditions, especially chronic liver diseases, can lead to cirrhosis in children and
adolescents. Most cases in clinical practice are caused by similar etiologies. In infants …

Background & Aims Primary prophylaxis of bleeding is debated for children with portal
hypertension because of the limited number of studies on its safety and efficacy, the lack of a …

Cavernous transformation of the portal vein (CTPV) is a sequela of extrahepatic and/or
intrahepatic portal vein obstruction caused by a combination of local and risk factors. It was …

While liver involvement is common in cystic fibrosis, the major liver disorder with impact on
the clinical outcome of individuals with CF is the development of multilobular cirrhosis with …