Pediatric low-grade glioma in the era of molecular diagnostics

S Ryall, U Tabori, C Hawkins - Acta neuropathologica communications, 2020 - Springer
Low grade gliomas are the most frequent brain tumors in children and encompass a
spectrum of histologic entities which are currently assigned World Health Organisation …

MAPK pathway activation in pilocytic astrocytoma

DTW Jones, J Gronych, P Lichter, O Witt… - Cellular and Molecular …, 2012 - Springer
Pilocytic astrocytoma (PA) is the most common tumor of the pediatric central nervous system
(CNS). A body of research over recent years has demonstrated a key role for mitogen …

Whole-genome sequencing identifies genetic alterations in pediatric low-grade gliomas

Nature genetics, 2013 - nature.com
The most common pediatric brain tumors are low-grade gliomas (LGGs). We used whole-
genome sequencing to identify multiple new genetic alterations involving BRAF, RAF1 …

BRAF Mutation and CDKN2A Deletion Define a Clinically Distinct Subgroup of Childhood Secondary High-Grade Glioma

M Mistry, N Zhukova, D Merico… - Journal of clinical …, 2015 - ascopubs.org
Purpose To uncover the genetic events leading to transformation of pediatric low-grade
glioma (PLGG) to secondary high-grade glioma (sHGG). Patients and Methods We …

BRAF-KIAA1549 Fusion Predicts Better Clinical Outcome in Pediatric Low-Grade Astrocytoma

C Hawkins, E Walker, N Mohamed, C Zhang… - Clinical Cancer …, 2011 - AACR
Purpose: Recent studies have revealed that the majority of pediatric low-grade astrocytomas
(PLGA) harbor the BRAF-KIAA1549 (BK) fusion gene resulting in constitutive activation of …

Molecularly defined diffuse leptomeningeal glioneuronal tumor (DLGNT) comprises two subgroups with distinct clinical and genetic features

MY Deng, M Sill, J Chiang, J Schittenhelm… - Acta …, 2018 - Springer
Diffuse leptomeningeal glioneuronal tumors (DLGNT) represent rare CNS neoplasms which
have been included in the 2016 update of the WHO classification. The wide spectrum of …

Genomic analysis of diffuse pediatric low-grade gliomas identifies recurrent oncogenic truncating rearrangements in the transcription factor MYBL1

LA Ramkissoon, PM Horowitz… - Proceedings of the …, 2013 - National Acad Sciences
Pediatric low-grade gliomas (PLGGs) are among the most common solid tumors in children
but, apart from BRAF kinase mutations or duplications in specific subclasses, few genetic …

Clinicopathological relevance of BRAF mutations in human cancer

S Pakneshan, A Salajegheh, RA Smith… - Pathology-Journal of …, 2013 - journals.lww.com
BRAF represents one of the most frequently mutated protein kinase genes in human
tumours. The mutation is commonly tested in pathology practice. BRAF mutation is seen in …

The oncogenic fusion landscape in pediatric CNS neoplasms

M Roosen, Z Odé, J Bunt, M Kool - Acta Neuropathologica, 2022 - Springer
Pediatric neoplasms in the central nervous system (CNS) are the leading cause of cancer-
related deaths in children. Recent developments in molecular analyses have greatly …

Pleomorphic xanthoastrocytoma: a brief review

N Shaikh, N Brahmbhatt, TJ Kruser, KL Kam… - CNS …, 2019 - Taylor & Francis
Pleomorphic xanthoastrocytoma (PXA) is a rare primary CNS tumor. Recent advances in the
molecular characterization are hel** to define subtypes of tumor. The discovery of BRAF …