Role of skeletal muscle in insulin resistance and glucose uptake

KE Merz, DC Thurmond - Comprehensive Physiology, 2011 - Wiley Online Library
The skeletal muscle is the largest organ in the body, by mass. It is also the regulator of
glucose homeostasis, responsible for 80% of postprandial glucose uptake from the …

[HTML][HTML] Immunobiology of inherited muscular dystrophies

JG Tidball, SS Welc… - Comprehensive …, 2018 - ncbi.nlm.nih.gov
The immune response to acute muscle damage is important for normal repair. However, in
chronic diseases such as many muscular dystrophies, the immune response can amplify …

[HTML][HTML] p38 MAPKs—roles in skeletal muscle physiology, disease mechanisms, and as potential therapeutic targets

CM Brennan, CP Emerson Jr, J Owens, N Christoforou - JCI insight, 2021 - ncbi.nlm.nih.gov
Abstract p38 MAPKs play a central role in orchestrating the cellular response to stress and
inflammation and in the regulation of myogenesis. Potent inhibitors of p38 MAPKs have …

Oxidative stress and pathology in muscular dystrophies: focus on protein thiol oxidation and dysferlinopathies

JR Terrill, HG Radley‐Crabb, T Iwasaki… - The FEBS …, 2013 - Wiley Online Library
The muscular dystrophies comprise more than 30 clinical disorders that are characterized by
progressive skeletal muscle wasting and degeneration. Although the genetic basis for many …

[HTML][HTML] Interplay between mitochondrial reactive oxygen species, oxidative stress and hypoxic adaptation in facioscapulohumeral muscular dystrophy: Metabolic …

P Heher, M Ganassi, A Weidinger, EN Engquist… - Redox biology, 2022 - Elsevier
Facioscapulohumeral muscular dystrophy (FSHD) is characterised by descending skeletal
muscle weakness and wasting. FSHD is caused by mis-expression of the transcription factor …

Pathomechanisms and biomarkers in facioscapulohumeral muscular dystrophy: roles of DUX4 and PAX7

CRS Banerji, PS Zammit - EMBO molecular medicine, 2021 - embopress.org
Facioscapulohumeral muscular dystrophy (FSHD) is characterised by progressive skeletal
muscle weakness and wasting. FSHD is linked to epigenetic derepression of the …

DUX4 role in normal physiology and in FSHD muscular dystrophy

E Mocciaro, V Runfola, P Ghezzi, M Pannese… - Cells, 2021 - mdpi.com
In the last decade, the sequence-specific transcription factor double homeobox 4 (DUX4)
has gone from being an obscure entity to being a key factor in important physiological and …

Facioscapulohumeral muscular dystrophy: genetics, gene activation and downstream signalling with regard to recent therapeutic approaches: an update

T Schätzl, L Kaiser, HP Deigner - Orphanet Journal of Rare Diseases, 2021 - Springer
Whilst a disease-modifying treatment for Facioscapulohumeral muscular dystrophy (FSHD)
does not exist currently, recent advances in complex molecular pathophysiology studies of …

A human pluripotent stem cell model of facioscapulohumeral muscular dystrophy-affected skeletal muscles

L Caron, D Kher, KL Lee, R McKernan… - Stem Cells …, 2016 - academic.oup.com
Facioscapulohumeral muscular dystrophy (FSHD) represents a major unmet clinical need
arising from the progressive weakness and atrophy of skeletal muscles. The dearth of …

DUX4-induced dsRNA and MYC mRNA stabilization activate apoptotic pathways in human cell models of facioscapulohumeral dystrophy

SC Shadle, JW Zhong, AE Campbell, ML Conerly… - PLoS …, 2017 - journals.plos.org
Facioscapulohumeral dystrophy (FSHD) is caused by the mis-expression of DUX4 in
skeletal muscle cells. DUX4 is a transcription factor that activates genes normally associated …