Pathomechanisms of blood‐brain barrier disruption in ALS

N Kakaroubas, S Brennan, M Keon… - Neuroscience …, 2019 - Wiley Online Library
The blood‐brain barrier (BBB) and the blood‐spinal cord barrier (BSCB) are responsible for
controlling the microenvironment within neural tissues in humans. These barriers are …

From basic research to the clinic: innovative therapies for ALS and FTD in the pipeline

RM Liscic, A Alberici, NJ Cairns, M Romano… - Molecular …, 2020 - Springer
Amyotrophic lateral sclerosis (ALS) and Frontotemporal Degeneration (FTD) are
neurodegenerative disorders, related by deterioration of motor and cognitive functions and …

Phase II trial of CoQ10 for ALS finds insufficient evidence to justify phase III

P Kaufmann, JLP Thompson, G Levy… - Annals of Neurology …, 2009 - Wiley Online Library
Objective Amyotrophic lateral sclerosis (ALS) is a devastating, and currently incurable,
neuromuscular disease in which oxidative stress and mitochondrial impairment are …

[HTML][HTML] Gastrostomy in patients with amyotrophic lateral sclerosis (ProGas): a prospective cohort study

ProGas Study Group - The Lancet Neurology, 2015 - Elsevier
Background Gastrostomy feeding is commonly used to support patients with amyotrophic
lateral sclerosis who develop severe dysphagia. Although recommended by both the …

Weight loss, dysphagia and supplement intake in patients with amyotrophic lateral sclerosis (ALS): impact on quality of life and therapeutic options

S Körner, M Hendricks, K Kollewe, A Zapf, R Dengler… - BMC neurology, 2013 - Springer
Background Weight loss is a frequent feature in the motor neuron disease Amyotrophic
lateral sclerosis (ALS). In this study we investigated possible causes of weight loss in ALS …

Nutrient effects on motor neurons and the risk of amyotrophic lateral sclerosis

PS Goncharova, TK Davydova, TE Popova… - Nutrients, 2021 - mdpi.com
Amyotrophic lateral sclerosis (ALS) is an incurable chronic progressive neurodegenerative
disease with the progressive degeneration of motor neurons in the motor cortex and lower …

Nutritional and metabolic support in patients with amyotrophic lateral sclerosis

M Muscaritoli, I Kushta, A Molfino, M Inghilleri… - Nutrition, 2012 - Elsevier
Amyotrophic lateral sclerosis (ALS) is the most common form of progressive motor neuron
disease and the most devastating neurodegenerative disorder. ALS is characterized by …

Integrated omic analysis delineates pathways modulating toxic TDP-43 protein aggregates in amyotrophic lateral sclerosis

S Rajaratnam, AP Soman, KS Phalguna, SS Pradhan… - Cells, 2023 - mdpi.com
Amyotrophic lateral sclerosis (ALS) is a multi-systemic, incurable, amyloid disease affecting
the motor neurons, resulting in the death of patients. The disease is either sporadic or …

[HTML][HTML] Body mass index and dietary intervention: implications for prognosis of amyotrophic lateral sclerosis

ST Ngo, FJ Steyn, PA McCombe - Journal of the neurological sciences, 2014 - Elsevier
Amyotrophic lateral sclerosis (ALS) is an adult onset, neurodegenerative disease that is
characterized by the loss of upper (corticospinal) and lower motor neurons. ALS is a …

Gastrostomy use in motor neurone disease (MND): a review, meta-analysis and survey of current practice

T Stavroulakis, T Walsh, PJ Shaw… - … Lateral Sclerosis and …, 2013 - Taylor & Francis
Gastrostomy feeding is commonly used to support MND patients with dysphagia. In this
paper we review three main methods of gastrostomy insertion (PEG, RIG, PIG); conduct a …