[HTML][HTML] The canonical Notch signaling pathway: unfolding the activation mechanism

R Kopan, MXG Ilagan - Cell, 2009 - cell.com
Notch signaling regulates many aspects of metazoan development and tissue renewal.
Accordingly, the misregulation or loss of Notch signaling underlies a wide range of human …

Trafficking and proteolytic processing of APP

C Haass, C Kaether… - Cold Spring …, 2012 - perspectivesinmedicine.cshlp.org
Accumulations of insoluble deposits of amyloid β-peptide are major pathological hallmarks
of Alzheimer disease. Amyloid β-peptide is derived by sequential proteolytic processing from …

The secretases: enzymes with therapeutic potential in Alzheimer disease

B De Strooper, R Vassar, T Golde - Nature reviews neurology, 2010 - nature.com
The amyloid hypothesis has yielded a series of well-validated candidate drug targets with
potential for the treatment of Alzheimer disease (AD). Three proteases that are involved in …

The mechanism of γ‐secretase dysfunction in familial Alzheimer disease

L Chávez‐Gutiérrez, L Bammens, I Benilova… - The EMBO …, 2012 - embopress.org
The mechanisms by which mutations in the presenilins (PSEN) or the amyloid precursor
protein (APP) genes cause familial Alzheimer disease (FAD) are controversial. FAD …

The many substrates of presenilin/γ-secretase

A Haapasalo, DM Kovacs - Journal of Alzheimer's disease, 2011 - content.iospress.com
The Alzheimer's disease (AD)-associated amyloid-β protein precursor (AβPP) is cleaved by
α-, β-, and presenilin (PS)/γ-secretases through sequential regulated proteolysis. These …

γ-Secretase directly sheds the survival receptor BCMA from plasma cells

SA Laurent, FS Hoffmann, PH Kuhn, Q Cheng… - Nature …, 2015 - nature.com
Survival of plasma cells is regulated by B-cell maturation antigen (BCMA), a membrane-
bound receptor activated by its agonist ligands BAFF and APRIL. Here we report that γ …

Proteases and proteolysis in Alzheimer disease: a multifactorial view on the disease process

B De Strooper - Physiological reviews, 2010 - journals.physiology.org
Alzheimer disease is characterized by the accumulation of abnormally folded protein
fragments, ie, amyloid beta peptide (Aβ) and tau that precipitate in amyloid plaques and …

Proteolytic processing of Alzheimer's β‐amyloid precursor protein

H Zhang, Q Ma, Y Zhang, H Xu - Journal of Neurochemistry …, 2012 - Wiley Online Library
J. Neurochem.(2012) 120 (Suppl. 1), 9–21. Abstract β‐Amyloid precursor protein (APP) is a
critical factor in the pathogenesis of Alzheimer's disease (AD). APP undergoes post …

[HTML][HTML] Making the final cut: pathogenic amyloid-β peptide generation by γ-secretase

H Steiner, A Fukumori, S Tagami, M Okochi - Cell Stress, 2018 - ncbi.nlm.nih.gov
Alzheimers disease (AD) is a devastating neurodegenerative disease of the elderly
population. Genetic evidence strongly suggests that aberrant generation and/or clearance of …

Regulated intramembrane proteolysis–lessons from amyloid precursor protein processing

SF Lichtenthaler, C Haass… - Journal of …, 2011 - Wiley Online Library
J. Neurochem.(2011) 117, 779–796. Abstract Regulated intramembrane proteolysis (RIP)
controls the communication between cells and the extracellular environment. RIP is …