Oxidative stress in neurodegenerative diseases

E Niedzielska, I Smaga, M Gawlik, A Moniczewski… - Molecular …, 2016 - Springer
The pathophysiologies of neurodegenerative diseases, including amyotrophic lateral
sclerosis (ALS), Parkinson's disease (PD), and Alzheimer's disease (AD), are far from being …

Redox dysregulation as a driver for DNA damage and its relationship to neurodegenerative diseases

S Shadfar, S Parakh, MS Jamali, JD Atkin - Translational …, 2023 - Springer
Redox homeostasis refers to the balance between the production of reactive oxygen species
(ROS) as well as reactive nitrogen species (RNS), and their elimination by antioxidants. It is …

Metabolomics of human brain aging and age-related neurodegenerative diseases

M Jové, M Portero-Otín, A Naudí, I Ferrer… - … of Neuropathology & …, 2014 - academic.oup.com
Neurons in the mature human central nervous system (CNS) perform a wide range of motor,
sensory, regulatory, behavioral, and cognitive functions. Such diverse functional output …

C9ORF72 GGGGCC Expanded Repeats Produce Splicing Dysregulation which Correlates with Disease Severity in Amyotrophic Lateral Sclerosis

J Cooper-Knock, JJ Bury, PR Heath, M Wyles… - PloS one, 2015 - journals.plos.org
Objective An intronic GGGGCC-repeat expansion of C9ORF72 is the most common genetic
variant of amyotrophic lateral sclerosis (ALS) and frontotemporal dementia. The mechanism …

SOD1 in ALS: taking stock in pathogenic mechanisms and the role of glial and muscle cells

C Peggion, V Scalcon, ML Massimino, K Nies… - Antioxidants, 2022 - mdpi.com
Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disorder characterized by
the loss of motor neurons in the brain and spinal cord. While the exact causes of ALS are still …

The unfolded protein response and the role of protein disulfide isomerase in neurodegeneration

ER Perri, CJ Thomas, S Parakh… - Frontiers in cell and …, 2016 - frontiersin.org
The maintenance and regulation of proteostasis is a critical function for post-mitotic neurons
and its dysregulation is increasingly implicated in neurodegenerative diseases. Despite …

Alterations in lipid metabolism of spinal cord linked to amyotrophic lateral sclerosis

AB Chaves-Filho, IFD Pinto, LS Dantas, AM Xavier… - Scientific reports, 2019 - nature.com
Amyotrophic lateral sclerosis (ALS) is characterized by progressive loss of upper and lower
motor neurons leading to muscle paralysis and death. While a link between dysregulated …

The NRF2-dependent transcriptional regulation of antioxidant defense pathways: Relevance for cell type-specific vulnerability to neurodegeneration and therapeutic …

SM Boas, KL Joyce, RM Cowell - Antioxidants, 2021 - mdpi.com
Oxidative stress has been implicated in the etiology and pathobiology of various
neurodegenerative diseases. At baseline, the cells of the nervous system have the capability …

Impact of reactive species on amino acids—biological relevance in proteins and induced pathologies

CMC Andrés, JM Pérez de la Lastra… - International Journal of …, 2022 - mdpi.com
This review examines the impact of reactive species RS (of oxygen ROS, nitrogen RNS and
halogens RHS) on various amino acids, analyzed from a reactive point of view of how during …

Panel of oxidative stress and inflammatory biomarkers in ALS: a pilot study

H Blasco, G Garcon, F Patin… - Canadian Journal of …, 2017 - cambridge.org
Background: Pathophysiological mechanisms that contribute to neurodegeneration in
Amyotrophic Lateral Sclerosis (ALS) include oxidative stress and inflammation. We …