Juvenile idiopathic arthritis: from aetiopathogenesis to therapeutic approaches

LN Zaripova, A Midgley, SE Christmas… - Pediatric …, 2021‏ - Springer
Juvenile idiopathic arthritis (JIA) is the most common paediatric rheumatological disorder
and is classified by subtype according to International League of Associations for …

[HTML][HTML] Silencing the cytokine storm: the use of intravenous anakinra in haemophagocytic lymphohistiocytosis or macrophage activation syndrome

P Mehta, RQ Cron, J Hartwell, JJ Manson… - The Lancet …, 2020‏ - thelancet.com
The term cytokine storm syndromes describes conditions characterised by a life-threatening,
fulminant hypercytokinaemia with high mortality. Cytokine storm syndromes can be genetic …

2021 American College of Rheumatology guideline for the treatment of juvenile idiopathic arthritis: therapeutic approaches for oligoarthritis, temporomandibular joint …

KB Onel, DB Horton, DJ Lovell, S Shenoi… - Arthritis & …, 2022‏ - Wiley Online Library
Objective To provide updated guidelines for pharmacologic management of juvenile
idiopathic arthritis (JIA), focusing on treatment of oligoarthritis, temporomandibular joint …

The 2022 EULAR/ACR points to consider at the early stages of diagnosis and management of suspected haemophagocytic lymphohistiocytosis/macrophage …

B Shakoory, A Geerlinks, M Wilejto, K Kernan… - Annals of the rheumatic …, 2023‏ - Elsevier
Objective Haemophagocytic lymphohistiocytosis (HLH) and macrophage activation
syndrome (MAS) are life-threatening systemic hyperinflammatory syndromes that can …

The IL-1 family of cytokines and receptors in rheumatic diseases

CA Dinarello - Nature Reviews Rheumatology, 2019‏ - nature.com
More than any other cytokine family, the 11 members of the IL-1 family are associated with
innate immune responses, which occur in acute inflammation and chronic inflammatory …

Hemophagocytic lymphohistiocytosis: an update on pathogenesis, diagnosis, and therapy

G Griffin, S Shenoi, GC Hughes - Best Practice & Research Clinical …, 2020‏ - Elsevier
Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening state of immune
hyperactivation that arises in the setting of genetic mutations and infectious, inflammatory, or …

Efficacy and safety of emapalumab in macrophage activation syndrome

F De Benedetti, AA Grom, PA Brogan… - Annals of the Rheumatic …, 2023‏ - Elsevier
Objectives Macrophage activation syndrome (MAS) is a severe, life-threatening complication
of systemic juvenile idiopathic arthritis (sJIA) and adult-onset Still's disease (AOSD). The …

Overview: systemic inflammatory response derived from lung injury caused by SARS-CoV-2 infection explains severe outcomes in COVID-19

RB Polidoro, RS Hagan, R de Santis Santiago… - Frontiers in …, 2020‏ - frontiersin.org
Most SARS-CoV2 infections will not develop into severe COVID-19. However, in some
patients, lung infection leads to the activation of alveolar macrophages and lung epithelial …

Interleukin-1 receptor blockade is associated with reduced mortality in sepsis patients with features of macrophage activation syndrome: reanalysis of a prior phase III …

B Shakoory, JA Carcillo, WW Chatham… - Critical care …, 2016‏ - journals.lww.com
Objective: To determine the efficacy of anakinra (recombinant interleukin-1 receptor
antagonist) in improving 28-day survival in sepsis patients with features of macrophage …

Benefit of anakinra in treating pediatric secondary hemophagocytic lymphohistiocytosis

EM Eloseily, P Weiser, CB Crayne… - Arthritis & …, 2020‏ - Wiley Online Library
Objective To assess the benefit of the recombinant human interleukin‐1 receptor antagonist
anakinra in treating pediatric patients with secondary hemophagocytic lymphohistiocytosis …