Diverse functions of cytochrome c in cell death and disease

Z Zhou, T Arroum, X Luo, R Kang, YJ Lee… - Cell Death & …, 2024‏ - nature.com
The redox-active protein cytochrome c is a highly positively charged hemoglobin that
regulates cell fate decisions of life and death. Under normal physiological conditions …

Mitochondrial dysfunction in inherited renal disease and acute kidney injury

F Emma, G Montini, SM Parikh, L Salviati - Nature Reviews Nephrology, 2016‏ - nature.com
Mitochondria are increasingly recognized as key players in genetic and acquired renal
diseases. Most mitochondrial cytopathies that cause renal symptoms are characterized by …

[HTML][HTML] Tissue-specific regulation of cytochrome c by post-translational modifications: respiration, the mitochondrial membrane potential, ROS, and apoptosis

HA Kalpage, V Bazylianska, MA Recanati… - The FASEB …, 2018‏ - pmc.ncbi.nlm.nih.gov
Cytochrome c (Cytc) plays a vital role in the mitochondrial electron transport chain (ETC). In
addition, it is a key regulator of apoptosis. Cytc has multiple other functions including ROS …

Multifunctional Cytochrome c: Learning New Tricks from an Old Dog

D Alvarez-Paggi, L Hannibal, MA Castro… - Chemical …, 2017‏ - ACS Publications
Cytochrome c (cyt c) is a small soluble heme protein characterized by a relatively flexible
structure, particularly in the ferric form, such that it is able to sample a broad conformational …

Interpreting the developmental dance of the megakaryocyte: a review of the cellular and molecular processes mediating platelet formation

KR Machlus, JN Thon… - British journal of …, 2014‏ - Wiley Online Library
Platelets are essential for haemostasis, and thrombocytopenia (platelet counts< 150× 109/l)
is a major clinical problem encountered across a number of conditions, including immune …

Inherited platelet disorders: an updated overview

V Palma-Barqueros, N Revilla, A Sánchez… - International journal of …, 2021‏ - mdpi.com
Platelets play a major role in hemostasis as ppwell as in many other physiological and
pathological processes. Accordingly, production of about 1011 platelet per day as well as …

Mutations in the 5′ UTR of ANKRD26, the ankirin repeat domain 26 gene, cause an autosomal-dominant form of inherited thrombocytopenia, THC2

T Pippucci, A Savoia, S Perrotta, N Pujol-Moix… - The American Journal of …, 2011‏ - cell.com
THC2, an autosomal-dominant thrombocytopenia described so far in only two families, has
been ascribed to mutations in MASTL or ACBD5. Here, we show that ANKRD26, another …

Apoptosis in megakaryocytes and platelets: the life and death of a lineage

K McArthur, S Chappaz, BT Kile - Blood, The Journal of the …, 2018‏ - ashpublications.org
Despite their profoundly different cellular composition, size, and function, megakaryocytes
and platelets both depend on restraint of the intrinsic (or “mitochondrial”) apoptosis pathway …

Hereditary thrombocytopenias: a growing list of disorders

P Noris, A Pecci - Hematology 2014, the American Society of …, 2017‏ - ashpublications.org
The introduction of high throughput sequencing (HTS) techniques greatly improved the
knowledge of inherited thrombocytopenias (ITs) over the last few years. A total of 33 different …

Inherited platelet disorders: toward DNA-based diagnosis

C Lentaigne, K Freson, MA Laffan… - Blood, The Journal …, 2016‏ - ashpublications.org
Variations in platelet number, volume, and function are largely genetically controlled, and
many loci associated with platelet traits have been identified by genome-wide association …